BIOMAT Database Logo BIOMAT Database Logo

Glycogen storage disease type I: effect of continuous nocturnal nasogastric feeding. 1978

A G Davidson, and L T Wong, and L Kirby, and W J Tze, and J M Rigg, and D A Applegarth

UI MeSH Term Description Entries
D007223 Infant A child between 1 and 23 months of age. Infants
D008297 Male Males
D002648 Child A person 6 to 12 years of age. An individual 2 to 5 years old is CHILD, PRESCHOOL. Children
D004750 Enteral Nutrition Nutritional support given via the alimentary canal or any route connected to the gastrointestinal system (i.e., the enteral route). This includes oral feeding, sip feeding, and tube feeding using nasogastric, gastrostomy, and jejunostomy tubes. Enteral Feeding,Force Feeding,Nutrition, Enteral,Tube Feeding,Gastric Feeding Tubes,Feeding Tube, Gastric,Feeding Tubes, Gastric,Feeding, Enteral,Feeding, Force,Feeding, Tube,Feedings, Force,Force Feedings,Gastric Feeding Tube,Tube, Gastric Feeding,Tubes, Gastric Feeding
D005526 Food, Formulated Food and dietary formulations including elemental (chemically defined formula) diets, synthetic and semisynthetic diets, space diets, weight-reduction formulas, tube-feeding diets, complete liquid diets, and supplemental liquid and solid diets. Diet, Chemically Defined,Diet, Elemental,Diet, Formula,Diet, Synthetic,Dietary Formulations,Chemically Defined Diet,Synthetic Diet,Chemically Defined Diets,Dietary Formulation,Diets, Chemically Defined,Diets, Elemental,Diets, Formula,Diets, Synthetic,Elemental Diet,Elemental Diets,Foods, Formulated,Formulated Food,Formulated Foods,Formulation, Dietary,Formulations, Dietary
D005690 Galactose An aldohexose that occurs naturally in the D-form in lactose, cerebrosides, gangliosides, and mucoproteins. Deficiency of galactosyl-1-phosphate uridyltransferase (GALACTOSE-1-PHOSPHATE URIDYL-TRANSFERASE DEFICIENCY DISEASE) causes an error in galactose metabolism called GALACTOSEMIA, resulting in elevations of galactose in the blood. D-Galactose,Galactopyranose,Galactopyranoside,D Galactose
D005934 Glucagon A 29-amino acid pancreatic peptide derived from proglucagon which is also the precursor of intestinal GLUCAGON-LIKE PEPTIDES. Glucagon is secreted by PANCREATIC ALPHA CELLS and plays an important role in regulation of BLOOD GLUCOSE concentration, ketone metabolism, and several other biochemical and physiological processes. (From Gilman et al., Goodman and Gilman's The Pharmacological Basis of Therapeutics, 9th ed, p1511) Glucagon (1-29),Glukagon,HG-Factor,Hyperglycemic-Glycogenolytic Factor,Proglucagon (33-61),HG Factor,Hyperglycemic Glycogenolytic Factor
D005947 Glucose A primary source of energy for living organisms. It is naturally occurring and is found in fruits and other parts of plants in its free state. It is used therapeutically in fluid and nutrient replacement. Dextrose,Anhydrous Dextrose,D-Glucose,Glucose Monohydrate,Glucose, (DL)-Isomer,Glucose, (alpha-D)-Isomer,Glucose, (beta-D)-Isomer,D Glucose,Dextrose, Anhydrous,Monohydrate, Glucose
D005951 Glucose Tolerance Test A test to determine the ability of an individual to maintain HOMEOSTASIS of BLOOD GLUCOSE. It includes measuring blood glucose levels in a fasting state, and at prescribed intervals before and after oral glucose intake (75 or 100 g) or intravenous infusion (0.5 g/kg). Intravenous Glucose Tolerance,Intravenous Glucose Tolerance Test,OGTT,Oral Glucose Tolerance,Oral Glucose Tolerance Test,Glucose Tolerance Tests,Glucose Tolerance, Oral
D005953 Glycogen Storage Disease Type I An autosomal recessive disease in which gene expression of glucose-6-phosphatase is absent, resulting in hypoglycemia due to lack of glucose production. Accumulation of glycogen in liver and kidney leads to organomegaly, particularly massive hepatomegaly. Increased concentrations of lactic acid and hyperlipidemia appear in the plasma. Clinical gout often appears in early childhood. Glucose-6-Phosphatase Deficiency,Glucosephosphatase Deficiency,Glycogenosis 1,Hepatorenal Glycogen Storage Disease,von Gierke Disease,Deficiency, Glucosephosphatase,Gierke Disease,Gierke's Disease,Glycogen Storage Disease 1 (GSD I),von Gierke's Disease,Deficiencies, Glucose-6-Phosphatase,Deficiencies, Glucosephosphatase,Deficiency, Glucose-6-Phosphatase,Disease, Gierke,Disease, Gierke's,Disease, von Gierke,Disease, von Gierke's,Gierkes Disease,Glucose 6 Phosphatase Deficiency,Glucose-6-Phosphatase Deficiencies,Glucosephosphatase Deficiencies,von Gierkes Disease

Related Publications

A G Davidson, and L T Wong, and L Kirby, and W J Tze, and J M Rigg, and D A Applegarth
Continuous nocturnal intragastric feeding for management of type 1 glycogen-storage disease.
February 1976, The New England journal of medicine,
A G Davidson, and L T Wong, and L Kirby, and W J Tze, and J M Rigg, and D A Applegarth
Amino acid and hormonal response to long-term nocturnal nasogastric feeding therapy of glycogen storage disease type I (GSD-I).
January 1978, Monographs in human genetics,
A G Davidson, and L T Wong, and L Kirby, and W J Tze, and J M Rigg, and D A Applegarth
Type I glycogen storage disease: five years of management with nocturnal intragastric feeding.
March 1980, The Journal of pediatrics,
A G Davidson, and L T Wong, and L Kirby, and W J Tze, and J M Rigg, and D A Applegarth
Resolution of the need for continuous nocturnal feeding in a patient with severe type I glycogen storage disease.
October 1981, The Journal of pediatrics,
A G Davidson, and L T Wong, and L Kirby, and W J Tze, and J M Rigg, and D A Applegarth
Circulating lipids and lipoproteins in glycogen storage disease type I with nocturnal intragastric feeding.
February 1988, Journal of lipid research,
A G Davidson, and L T Wong, and L Kirby, and W J Tze, and J M Rigg, and D A Applegarth
Letter: Nocturnal feeding for glycogen-storage disease.
May 1976, The New England journal of medicine,
A G Davidson, and L T Wong, and L Kirby, and W J Tze, and J M Rigg, and D A Applegarth
Dietary treatment of glycogen storage disease type Ia: uncooked cornstarch and/or continuous nocturnal gastric drip-feeding?
May 2013, Molecular genetics and metabolism,
A G Davidson, and L T Wong, and L Kirby, and W J Tze, and J M Rigg, and D A Applegarth
Successful treatment of severe type I glycogen storage disease with neonatal presentation by nocturnal intragastric feeding.
May 1979, The Journal of pediatrics,
A G Davidson, and L T Wong, and L Kirby, and W J Tze, and J M Rigg, and D A Applegarth
Glycogen storage disease: type I.
June 1969, American journal of diseases of children (1960),
A G Davidson, and L T Wong, and L Kirby, and W J Tze, and J M Rigg, and D A Applegarth
Glycogen storage disease: type I.
June 1969, American journal of diseases of children (1960),
Copied contents to your clipboard!