Ruptured aortic dissecting aneurysm in Turner's syndrome: a case report and review of literature. 2000

H Hirose, and A Amano, and A Takahashi, and N Nagano, and T Kohmoto
Department of Cardiovascular Surgery, Shin-Tokyo Hospital, Chiba, Japan.

Cardiovascular malformations are frequently observed in Turner's syndrome. Bicuspid aortic valve and coarctation of the aorta are commonly associated with Turner's syndrome whereas aortic dissection is rare but its rupture results in death. We experienced a case of ruptured dissecting aneurysm (Stanford type A) in a 30-year-old female with Turner's syndrome. Emergent total arch replacement was performed successfully. A literature review revealed 32 cases of aortic dissection in patients with Turner's syndrome, including 15 cases of rupture. However, survival after rupture was reported only two cases. To our knowledge, this report descries the third known case of successful surgical management of ruptured aortic dissection in Turner's syndrome.

UI MeSH Term Description Entries
D005260 Female Females
D006801 Humans Members of the species Homo sapiens. Homo sapiens,Man (Taxonomy),Human,Man, Modern,Modern Man
D000328 Adult A person having attained full growth or maturity. Adults are of 19 through 44 years of age. For a person between 19 and 24 years of age, YOUNG ADULT is available. Adults
D000784 Aortic Dissection A tear in the inner layer of the AORTA leading to interstitial HEMORRHAGE, and splitting (dissecting) of the aortic TUNICA MEDIA layer. It typically begins with a tear in the TUNICA INTIMA layer. Aneurysm, Dissecting,Aortic Dissecting Aneurysm,Dissecting Aneurysm,Dissecting Aneurysm Aorta,Aneurysm Aorta, Dissecting,Aneurysm, Aortic Dissecting,Aorta, Dissecting Aneurysm,Aortic Dissecting Aneurysms,Aortic Dissections,Dissecting Aneurysm Aortas,Dissecting Aneurysm, Aortic,Dissecting Aneurysms,Dissection, Aortic
D001019 Aortic Rupture The tearing or bursting of the wall along any portion of the AORTA, such as thoracic or abdominal. It may result from the rupture of an aneurysm or it may be due to TRAUMA. Aortic Aneurysm, Ruptured,Ruptured Aortic Aneurysm,Aneurysm, Ruptured Aortic,Aneurysms, Ruptured Aortic,Aortic Aneurysms, Ruptured,Aortic Ruptures,Rupture, Aortic,Ruptured Aortic Aneurysms,Ruptures, Aortic
D014424 Turner Syndrome A syndrome of defective gonadal development in phenotypic females associated with the karyotype 45,X (or 45,XO). Patients generally are of short stature with undifferentiated GONADS (streak gonads), SEXUAL INFANTILISM, HYPOGONADISM, webbing of the neck, cubitus valgus, elevated GONADOTROPINS, decreased ESTRADIOL level in blood, and CONGENITAL HEART DEFECTS. NOONAN SYNDROME (also called Pseudo-Turner Syndrome and Male Turner Syndrome) resembles this disorder; however, it occurs in males and females with a normal karyotype and is inherited as an autosomal dominant. Bonnevie-Ullrich Syndrome,Gonadal Dysgenesis, 45,X,Gonadal Dysgenesis, XO,Monosomy X,Status Bonnevie-Ullrich,Turner's Syndrome,Ullrich-Turner Syndrome,Bonnevie Ullrich Syndrome,Status Bonnevie Ullrich,Syndrome, Ullrich-Turner,Turners Syndrome,Ullrich Turner Syndrome,XO Gonadal Dysgenesis

Related Publications

H Hirose, and A Amano, and A Takahashi, and N Nagano, and T Kohmoto
January 2007, Surgery today,
H Hirose, and A Amano, and A Takahashi, and N Nagano, and T Kohmoto
July 1992, Archives des maladies du coeur et des vaisseaux,
H Hirose, and A Amano, and A Takahashi, and N Nagano, and T Kohmoto
January 1961, Revista de la Facultad de Ciencias Medicas de Cordoba,
H Hirose, and A Amano, and A Takahashi, and N Nagano, and T Kohmoto
January 1974, Archivos del Instituto de Cardiologia de Mexico,
H Hirose, and A Amano, and A Takahashi, and N Nagano, and T Kohmoto
September 1981, Clinical pediatrics,
H Hirose, and A Amano, and A Takahashi, and N Nagano, and T Kohmoto
July 1982, Postgraduate medical journal,
H Hirose, and A Amano, and A Takahashi, and N Nagano, and T Kohmoto
May 1982, Zeitschrift fur die gesamte innere Medizin und ihre Grenzgebiete,
H Hirose, and A Amano, and A Takahashi, and N Nagano, and T Kohmoto
January 1998, The Journal of emergency medicine,
H Hirose, and A Amano, and A Takahashi, and N Nagano, and T Kohmoto
November 1963, Proceedings of the Weekly Seminar in Neurology,
H Hirose, and A Amano, and A Takahashi, and N Nagano, and T Kohmoto
June 2021, Cureus,
Copied contents to your clipboard!