BIOMAT Database Logo BIOMAT Database Logo

Multicentric pheochromocytoma and involvement of the inferior vena cava. 2001

A M Lucon, and R Falci, and J N Praxedes, and M C Machado, and L B Saldanha, and M M Machado, and S Arap
Division of Urology, Department of Surgery, Faculty of Medicine, University of São Paulo, Brazil. webmaster@urologia.hcnet.usp.br

BACKGROUND Extension of pheochromocytomas to the inferior vena cava is rare. Multicentric tumors are rare as well, being present in up to 10% of cases. Surgery is the treatment of choice because of the long-term survival free of disease. METHODS Case report. METHODS We report on a case of right adrenal pheochromocytoma with extension to the supra-diaphragmatic vena cava, which underwent surgical excision through thoracophrenic laparotomy without the need for cardiopulmonary bypass. In a 6-year follow-up, another pheochromocytoma was found in the infra-renal Zuckerkandl's organ. Complete surgical excision of the tumor was performed by a median laparotomy and complete retroperitoneal dissection. In both cases, the total removal of the pheochromocytoma has been guaranteed by having margins free of tumor and a normal post-operative level of catecholamines. The pathological study revealed a malignant pheochromocytoma with margins free of neoplasia in both specimens.

UI MeSH Term Description Entries
D008297 Male Males
D009361 Neoplasm Invasiveness Ability of neoplasms to infiltrate and actively destroy surrounding tissue. Invasiveness, Neoplasm,Neoplasm Invasion,Invasion, Neoplasm
D010673 Pheochromocytoma A usually benign, well-encapsulated, lobular, vascular tumor of chromaffin tissue of the ADRENAL MEDULLA or sympathetic paraganglia. The cardinal symptom, reflecting the increased secretion of EPINEPHRINE and NOREPINEPHRINE, is HYPERTENSION, which may be persistent or intermittent. During severe attacks, there may be HEADACHE; SWEATING, palpitation, apprehension, TREMOR; PALLOR or FLUSHING of the face, NAUSEA and VOMITING, pain in the CHEST and ABDOMEN, and paresthesias of the extremities. The incidence of malignancy is as low as 5% but the pathologic distinction between benign and malignant pheochromocytomas is not clear. (Dorland, 27th ed; DeVita Jr et al., Cancer: Principles & Practice of Oncology, 3d ed, p1298) Pheochromocytoma, Extra-Adrenal,Extra-Adrenal Pheochromocytoma,Extra-Adrenal Pheochromocytomas,Pheochromocytoma, Extra Adrenal,Pheochromocytomas,Pheochromocytomas, Extra-Adrenal
D011859 Radiography Examination of any part of the body for diagnostic purposes by means of X-RAYS or GAMMA RAYS, recording the image on a sensitized surface (such as photographic film). Radiology, Diagnostic X-Ray,Roentgenography,X-Ray, Diagnostic,Diagnostic X-Ray,Diagnostic X-Ray Radiology,X-Ray Radiology, Diagnostic,Diagnostic X Ray,Diagnostic X Ray Radiology,Diagnostic X-Rays,Radiology, Diagnostic X Ray,X Ray Radiology, Diagnostic,X Ray, Diagnostic,X-Rays, Diagnostic
D006801 Humans Members of the species Homo sapiens. Homo sapiens,Man (Taxonomy),Human,Man, Modern,Modern Man
D000310 Adrenal Gland Neoplasms Tumors or cancer of the ADRENAL GLANDS. Adrenal Cancer,Adrenal Gland Cancer,Adrenal Neoplasm,Cancer of the Adrenal Gland,Neoplasms, Adrenal Gland,Adrenal Cancers,Adrenal Gland Cancers,Adrenal Gland Neoplasm,Adrenal Neoplasms,Cancer, Adrenal,Cancer, Adrenal Gland,Cancers, Adrenal,Cancers, Adrenal Gland,Neoplasm, Adrenal,Neoplasm, Adrenal Gland,Neoplasms, Adrenal
D000328 Adult A person having attained full growth or maturity. Adults are of 19 through 44 years of age. For a person between 19 and 24 years of age, YOUNG ADULT is available. Adults
D012186 Retroperitoneal Neoplasms New abnormal growth of tissue in the RETROPERITONEAL SPACE. Neoplasm, Retroperitoneal,Neoplasms, Retroperitoneal,Retroperitoneal Neoplasm
D014682 Vena Cava, Inferior The venous trunk which receives blood from the lower extremities and from the pelvic and abdominal organs. Inferior Vena Cava,Inferior Vena Cavas,Vena Cavas, Inferior

Related Publications

A M Lucon, and R Falci, and J N Praxedes, and M C Machado, and L B Saldanha, and M M Machado, and S Arap
[Neoplastic involvement of the inferior vena cava].
January 1994, Il Giornale di chirurgia,
A M Lucon, and R Falci, and J N Praxedes, and M C Machado, and L B Saldanha, and M M Machado, and S Arap
Pheochromocytoma invasion of the inferior vena cava: sonographic evaluation.
December 1983, Radiology,
A M Lucon, and R Falci, and J N Praxedes, and M C Machado, and L B Saldanha, and M M Machado, and S Arap
Adrenal tumors: involvement of the inferior vena cava.
November 1987, The Journal of urology,
A M Lucon, and R Falci, and J N Praxedes, and M C Machado, and L B Saldanha, and M M Machado, and S Arap
Pheochromocytoma with inferior vena cava thrombosis: An unusual association.
April 2012, Journal of cardiovascular disease research,
A M Lucon, and R Falci, and J N Praxedes, and M C Machado, and L B Saldanha, and M M Machado, and S Arap
Marker-Negative Pheochromocytoma Associated with Inferior Vena Cava Thrombosis.
January 2017, Case reports in urology,
A M Lucon, and R Falci, and J N Praxedes, and M C Machado, and L B Saldanha, and M M Machado, and S Arap
Inferior vena cava involvement by a phaeochromocytoma.
July 1987, The British journal of surgery,
A M Lucon, and R Falci, and J N Praxedes, and M C Machado, and L B Saldanha, and M M Machado, and S Arap
[Obstruction of inferior vena cava (vena cava inferior syndrome)].
January 1996, Ryoikibetsu shokogun shirizu,
A M Lucon, and R Falci, and J N Praxedes, and M C Machado, and L B Saldanha, and M M Machado, and S Arap
Pheochromocytoma with extension into the inferior vena cava: a case report.
April 1992, Surgery,
A M Lucon, and R Falci, and J N Praxedes, and M C Machado, and L B Saldanha, and M M Machado, and S Arap
Dual inferior vena cava: two inferior vena cava filters.
August 2007, The Annals of thoracic surgery,
A M Lucon, and R Falci, and J N Praxedes, and M C Machado, and L B Saldanha, and M M Machado, and S Arap
Renal sinus haemangioma with inferior vena cava involvement.
December 2003, BJU international,
Copied contents to your clipboard!