Idiopathic sclerosing encapsulating peritonitis: a case report. 2003

Giulio Carcano, and Francesca Rovera, and Luigi Boni, and Gianlorenzo Dionigi, and Laura Uccella, and Renzo Dionigi
Department of Surgery, University of Insubria, Azienda Ospedaliera Ospedale di Circolo, Varese.

Sclerosing encapsulating peritonitis is an uncommon but potentially lethal condition, which can lead to severe complications such as bowel obstruction, enterocutaneous fistualas and necrosis. The treatment is debated because of the high morbidity and mortality of the surgical approach. The aim of this study was to contribute to achieving a better approach to surgical treatment of sclerosing encapsulating peritonitis. This report describes an even rarer case of idiopathic sclerosing encapsulating peritonitis diagnosed intraoperatively, observed in the Insubria University Department of Surgery in Varese, Italy, where surgery was mandatory due to the sudden onset of the disease and lack of a definitive diagnosis. Temporary ileostomy and partial resection of the peritoneum were performed. At present (December 2002) the patient is alive and well. Management of sclerosing encapsulating peritonitis is controversial, but the surgical treatment should be as conservative as possible. Guidelines for the treatment of sclerosing encapsulating peritonitis are needed.

UI MeSH Term Description Entries
D008297 Male Males
D008875 Middle Aged An adult aged 45 - 64 years. Middle Age
D010538 Peritonitis INFLAMMATION of the PERITONEUM lining the ABDOMINAL CAVITY as the result of infectious, autoimmune, or chemical processes. Primary peritonitis is due to infection of the PERITONEAL CAVITY via hematogenous or lymphatic spread and without intra-abdominal source. Secondary peritonitis arises from the ABDOMINAL CAVITY itself through RUPTURE or ABSCESS of intra-abdominal organs. Primary Peritonitis,Secondary Peritonitis,Peritonitis, Primary,Peritonitis, Secondary
D006801 Humans Members of the species Homo sapiens. Homo sapiens,Man (Taxonomy),Human,Man, Modern,Modern Man

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