A case of a granular neuroma of the true vocal cord of a 47-year-old woman is presented. In world literature about 125 cases of this benign tumor in the larynx are published until now. The most common symptom of this tumor is hoarseness. The correct treatment is the total excision to avoid recurrence. The histology shows typical uniform cells, their cytoplasm filled with eosinophilic granules. The overlying epithelium may show pseudoepitheliomatous hyperplasia, which must not be misinterpreted as malignant squamous cell carcinoma. Finally the theory of Feyrter concerning the neurogenous origin of this tumor is discussed.