Biomaterial Database

Progressive facial hemiatrophy with localized scleroderma. 1992

A Nakazawa, and I Matsuo, and M Ohkido

Department of Dermatology, Tokai University School of Medicine, Kanagawa, Japan.

A 46-year-old woman who presented with progressive facial hemiatrophy (PFH) following localized scleroderma is described. The patient had a markedly deformed and depressed plaque surrounded by erythema on the right cheek. She also showed linear scleroderma with hair loss on the occipital area and morphea lesions on the neck and shoulder. Histological findings of the facial and other atrophic lesions were consistent with localized scleroderma. Therefore, the PFH and localized scleroderma may have had the same pathological background in this case.

UI	MeSH Term	Description	Entries
D008875	Middle Aged	An adult aged 45 - 64 years.	Middle Age
D005150	Facial Hemiatrophy	A syndrome characterized by slowly progressive unilateral atrophy of facial subcutaneous fat, muscle tissue, skin, cartilage, and bone. The condition typically progresses over a period of 2-10 years and then stabilizes.	Hemifacial Atrophy,Romberg Disease,Facial Hemiatrophy of Romberg,Hemifacial Atrophy, Progressive,Parry-Romberg Disease,Parry-Romberg Syndrome,Progressive Facial Hemiatrophy,Progressive Hemifacial Atrophy,Romberg Hemi-Facial Atrophy,Romberg's Disease,Atrophies, Hemifacial,Atrophies, Progressive Hemifacial,Atrophy, Hemifacial,Atrophy, Progressive Hemifacial,Atrophy, Romberg Hemi-Facial,Disease, Parry-Romberg,Disease, Romberg,Disease, Romberg's,Facial Hemiatrophies,Facial Hemiatrophies, Progressive,Facial Hemiatrophy, Progressive,Hemi-Facial Atrophy, Romberg,Hemiatrophies, Facial,Hemiatrophies, Progressive Facial,Hemiatrophy, Facial,Hemiatrophy, Progressive Facial,Hemifacial Atrophies,Parry Romberg Disease,Parry Romberg Syndrome,Progressive Facial Hemiatrophies,Progressive Hemifacial Atrophies,Romberg Facial Hemiatrophy,Romberg Hemi Facial Atrophy,Rombergs Disease,Syndrome, Parry-Romberg
D005260	Female		Females
D006801	Humans	Members of the species Homo sapiens.	Homo sapiens,Man (Taxonomy),Human,Man, Modern,Modern Man
D012594	Scleroderma, Localized	A term used to describe a variety of localized asymmetrical SKIN thickening that is similar to those of SYSTEMIC SCLERODERMA but without the disease features in the multiple internal organs and BLOOD VESSELS. Lesions may be characterized as patches or plaques (morphea), bands (linear), or nodules.	Dermatosclerosis,Morphea,Scleroderma, Circumscribed,Frontal Linear Scleroderma en Coup de Sabre,Linear Scleroderma,Scleroderma, Linear,Circumscribed Scleroderma,Localized Scleroderma,Morpheas,Sclerodermas, Localized