-transparent.png){kind=logo}
Three sisters with cystic dilatation of the intrahepatic bile ducts (Caroli's disease) are reported. The index case, a 41-year-old woman with remittent high fever and right upper quadrant abdominal pain, was diagnosed as Caroli's disease with hepatic lithiasis and cholangitis based on findings of ultrasonography, computed tomography and endoscopic retrograde cholangiography. Her two older sisters were also examined and found to have the same disease without clinical symptoms. Their symptoms, locations of the dilated ducts and complications all varied. The hereditary mode of Caroli's disease in 13 families (32 cases) reported in the world literature including our study was examined. While Caroli's disease is thought to be an autosomal recessive disease, a conclusion on the hereditary mode of transmission could not be made in this study because of an insufficient investigation of family members, especially the parents.
K Yoshizawa, and
K Kiyosawa, and
K Yabu, and
S Usuda, and
S Shimizu, and
Y Fujimori, and
K Mukawa, and
E Tanaka, and
T Sodeyama, and
S Furuta
July 1990,
The Korean journal of internal medicine,
K Yoshizawa, and
K Kiyosawa, and
K Yabu, and
S Usuda, and
S Shimizu, and
Y Fujimori, and
K Mukawa, and
E Tanaka, and
T Sodeyama, and
S Furuta
December 2002,
European journal of gastroenterology & hepatology,
K Yoshizawa, and
K Kiyosawa, and
K Yabu, and
S Usuda, and
S Shimizu, and
Y Fujimori, and
K Mukawa, and
E Tanaka, and
T Sodeyama, and
S Furuta
July 2002,
The American journal of gastroenterology,
K Yoshizawa, and
K Kiyosawa, and
K Yabu, and
S Usuda, and
S Shimizu, and
Y Fujimori, and
K Mukawa, and
E Tanaka, and
T Sodeyama, and
S Furuta
October 1966,
Danish medical bulletin,
K Yoshizawa, and
K Kiyosawa, and
K Yabu, and
S Usuda, and
S Shimizu, and
Y Fujimori, and
K Mukawa, and
E Tanaka, and
T Sodeyama, and
S Furuta
January 1994,
La Radiologia medica,
K Yoshizawa, and
K Kiyosawa, and
K Yabu, and
S Usuda, and
S Shimizu, and
Y Fujimori, and
K Mukawa, and
E Tanaka, and
T Sodeyama, and
S Furuta
January 1978,
Scandinavian journal of infectious diseases,
K Yoshizawa, and
K Kiyosawa, and
K Yabu, and
S Usuda, and
S Shimizu, and
Y Fujimori, and
K Mukawa, and
E Tanaka, and
T Sodeyama, and
S Furuta
September 1952,
The American journal of medicine,
K Yoshizawa, and
K Kiyosawa, and
K Yabu, and
S Usuda, and
S Shimizu, and
Y Fujimori, and
K Mukawa, and
E Tanaka, and
T Sodeyama, and
S Furuta
January 2003,
Acta medica Croatica : casopis Hravatske akademije medicinskih znanosti,
K Yoshizawa, and
K Kiyosawa, and
K Yabu, and
S Usuda, and
S Shimizu, and
Y Fujimori, and
K Mukawa, and
E Tanaka, and
T Sodeyama, and
S Furuta
August 2004,
Indian pediatrics,
K Yoshizawa, and
K Kiyosawa, and
K Yabu, and
S Usuda, and
S Shimizu, and
Y Fujimori, and
K Mukawa, and
E Tanaka, and
T Sodeyama, and
S Furuta
November 2006,
The Journal of the Association of Physicians of India,
