Biomaterial Database

[Pulmonary lymphangiomyomatosis associated with spontaneous pneumothorax]. 1992

G Okaniwa, and T Imai, and S Fujimura

Department of Chest Surgery, Aomori Prefectural Central Hospital, Japan.

A 34-year-old female associated with spontaneous pneumothorax was diagnosed as pulmonary lymphangiomyomatosis by open lung biopsy and pathological examination. The biopsy specimen of the lung showed marked proliferation of smooth muscle in the lung. This disease is seen only in women in childbearing age, and hormonal therapy is ineffective, but bilateral oophorectomy seems, in some cases, to have a beneficial effect. Lung transplantation can be applied to patients with terminal pulmonary lymphangiomyomatosis.

UI	MeSH Term	Description	Entries
D008175	Lung Neoplasms	Tumors or cancer of the LUNG.	Cancer of Lung,Lung Cancer,Pulmonary Cancer,Pulmonary Neoplasms,Cancer of the Lung,Neoplasms, Lung,Neoplasms, Pulmonary,Cancer, Lung,Cancer, Pulmonary,Cancers, Lung,Cancers, Pulmonary,Lung Cancers,Lung Neoplasm,Neoplasm, Lung,Neoplasm, Pulmonary,Pulmonary Cancers,Pulmonary Neoplasm
D008203	Lymphangiomyoma	A tumorlike condition characterized by SMOOTH MUSCLE and ENDOTHELIUM proliferation of LYMPHATIC VESSELS and LYMPH NODES in the MEDIASTINUM and retroperitoneum, also in the lung. It may be manifested by chylous PLEURAL EFFUSION and ASCITES.	Lymphangioleiomyoma,Lymphangioleiomyomas,Lymphangiomyomas
D011030	Pneumothorax	An accumulation of air or gas in the PLEURAL CAVITY, which may occur spontaneously or as a result of trauma or a pathological process. The gas may also be introduced deliberately during PNEUMOTHORAX, ARTIFICIAL.	Pneumothorax, Primary Spontaneous,Pressure Pneumothorax,Primary Spontaneous Pneumothorax,Spontaneous Pneumothorax,Tension Pneumothorax,Pneumothorax, Pressure,Pneumothorax, Spontaneous,Pneumothorax, Tension,Spontaneous Pneumothorax, Primary
D005260	Female		Females
D006801	Humans	Members of the species Homo sapiens.	Homo sapiens,Man (Taxonomy),Human,Man, Modern,Modern Man
D000328	Adult	A person having attained full growth or maturity. Adults are of 19 through 44 years of age. For a person between 19 and 24 years of age, YOUNG ADULT is available.	Adults