Marginal sinus arteriovenous fistulas mimicking carotid cavernous fistulas: diagnostic and therapeutic considerations. 2007

R D Turner, and V Gonugunta, and M E Kelly, and T J Masaryk, and D J Fiorella
Department of Neurosurgery, Cleveland Clinic Foundation, Cleveland, OH44195, USA. turnerr@ccf.org

Marginal sinus fistulas (MSFs) are uncommon vascular anomalies. Occasionally, the dominant venous drainage is forced retrograde up the inferior petrosal sinus and into the cavernous sinus, causing chemosis, proptosis, and ocular hypertension, mimicking a carotid cavernous fistula. This atypical clinical presentation may lead to misdiagnosis and inappropriate hazardous treatment of an MSF. Identifying the site of the fistula and understanding the anatomy of the venous drainage are critical in providing appropriate, safe, and efficacious endovascular treatment.

UI MeSH Term Description Entries
D008297 Male Males
D008875 Middle Aged An adult aged 45 - 64 years. Middle Age
D011859 Radiography Examination of any part of the body for diagnostic purposes by means of X-RAYS or GAMMA RAYS, recording the image on a sensitized surface (such as photographic film). Radiology, Diagnostic X-Ray,Roentgenography,X-Ray, Diagnostic,Diagnostic X-Ray,Diagnostic X-Ray Radiology,X-Ray Radiology, Diagnostic,Diagnostic X Ray,Diagnostic X Ray Radiology,Diagnostic X-Rays,Radiology, Diagnostic X Ray,X Ray Radiology, Diagnostic,X Ray, Diagnostic,X-Rays, Diagnostic
D002426 Cavernous Sinus An irregularly shaped venous space in the dura mater at either side of the sphenoid bone. Sinus, Cavernous
D003937 Diagnosis, Differential Determination of which one of two or more diseases or conditions a patient is suffering from by systematically comparing and contrasting results of diagnostic measures. Diagnoses, Differential,Differential Diagnoses,Differential Diagnosis
D004621 Embolization, Therapeutic A method of hemostasis utilizing various agents such as Gelfoam, silastic, metal, glass, or plastic pellets, autologous clot, fat, and muscle as emboli. It has been used in the treatment of spinal cord and INTRACRANIAL ARTERIOVENOUS MALFORMATIONS, renal arteriovenous fistulas, gastrointestinal bleeding, epistaxis, hypersplenism, certain highly vascular tumors, traumatic rupture of blood vessels, and control of operative hemorrhage. Embolotherapy,Therapeutic Embolization,Embolizations, Therapeutic,Embolotherapies,Therapeutic Embolizations
D006801 Humans Members of the species Homo sapiens. Homo sapiens,Man (Taxonomy),Human,Man, Modern,Modern Man
D000368 Aged A person 65 years of age or older. For a person older than 79 years, AGED, 80 AND OVER is available. Elderly
D020216 Carotid-Cavernous Sinus Fistula An acquired or spontaneous abnormality in which there is communication between CAVERNOUS SINUS, a venous structure, and the CAROTID ARTERIES. It is often associated with HEAD TRAUMA, specifically basilar skull fractures (SKULL FRACTURE, BASILAR). Clinical signs often include VISION DISORDERS and INTRACRANIAL HYPERTENSION. Caroticocavernous Fistula,Carotid Cavernous Fistula,Fistula, Carotid Artery-Cavernous Sinus,Traumatic Carotid-Cavernous Sinus Fistula,C-C Fistula,Carotid Artery-Cavernous Sinus Fistula,C-C Fistulas,Caroticocavernous Fistulas,Carotid Artery Cavernous Sinus Fistula,Carotid Cavernous Fistulas,Carotid Cavernous Sinus Fistula,Carotid-Cavernous Sinus Fistulas,Cavernous Fistula, Carotid,Fistula, C-C,Fistula, Caroticocavernous,Fistula, Carotid Artery Cavernous Sinus,Fistula, Carotid Cavernous,Fistula, Carotid-Cavernous Sinus,Traumatic Carotid Cavernous Sinus Fistula
D020785 Central Nervous System Vascular Malformations Congenital, inherited, or acquired abnormalities involving ARTERIES; VEINS; or venous sinuses in the BRAIN; SPINAL CORD; and MENINGES. CNS Vascular Malformations,Congenital Vascular Malformations, Central Nervous System,Vascular Malformations, Brain,Vascular Malformations, Central Nervous System,Capillary Telangiectasia, Brain,Central Nervous System Congenital Vascular Malformations,Central Nervous System Vascular Anomalies,Cerebral Embryonic Artery, Persistent,Dural Arteriovenous Fistula,Embryonic Artery, Persistent, Cerebral,Persistent Cerebral Embryonic Artery,Pontine Capillary Telangiectasias,Vascular Anomalies, Central Nervous System,Vascular Malformations, Congenital, Nervous System,Arteriovenous Fistula, Dural,Arteriovenous Fistulas, Dural,Brain Capillary Telangiectasia,Brain Capillary Telangiectasias,Brain Vascular Malformation,Brain Vascular Malformations,CNS Vascular Malformation,Capillary Telangiectasia, Pontine,Capillary Telangiectasias, Brain,Capillary Telangiectasias, Pontine,Dural Arteriovenous Fistulas,Malformation, Brain Vascular,Malformation, CNS Vascular,Malformations, Brain Vascular,Malformations, CNS Vascular,Pontine Capillary Telangiectasia,Telangiectasia, Brain Capillary,Telangiectasia, Pontine Capillary,Telangiectasias, Brain Capillary,Telangiectasias, Pontine Capillary,Vascular Malformation, Brain,Vascular Malformation, CNS,Vascular Malformations, CNS

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