Biomaterial Database

[Budd-Chiari syndrome--hematologists' part in the multidisciplinary approach]. 2008

P Dulícek, and J Malý

Oddĕlení klinické hematologie II. Interní kliniky Lékarské fakulty UK a FN Hradec Králové. PetrDulicek@seznam.cz

Budd-Chiari syndrome presents a serious disease with a complex etiology and clinical manifestations, which is associated with high morbidity and mortality. An early diagnosis and therapy is mandatory due to the severity of disease and therapy contains the treatment of underlying disorder, anticoagulation therapy and therapy of liver impairment. We discuss hematologists' contribution to the diagnostic approach and therapy of this syndrome.

UI	MeSH Term	Description	Entries
D006502	Budd-Chiari Syndrome	A condition in which the hepatic venous outflow is obstructed anywhere from the small HEPATIC VEINS to the junction of the INFERIOR VENA CAVA and the RIGHT ATRIUM. Usually the blockage is extrahepatic and caused by blood clots (THROMBUS) or fibrous webs. Parenchymal FIBROSIS is uncommon.	Chiari's Syndrome,Hepatic Venous Outflow Obstruction,Hepatic Vein Thrombosis,Budd Chiari Syndrome,Chiari Syndrome,Chiaris Syndrome,Hepatic Vein Thromboses,Thromboses, Hepatic Vein,Thrombosis, Hepatic Vein,Vein Thromboses, Hepatic,Vein Thrombosis, Hepatic
D006801	Humans	Members of the species Homo sapiens.	Homo sapiens,Man (Taxonomy),Human,Man, Modern,Modern Man
D019851	Thrombophilia	A disorder of HEMOSTASIS in which there is a tendency for the occurrence of THROMBOSIS.	Hypercoagulability,Hypercoagulabilities,Thrombophilias