BIOMAT Database Logo BIOMAT Database Logo

Congenital hepatic fibrosis, liver cell carcinoma and adult polycystic kidneys. 1977

J L Manes, and J M Kissane, and A J Valdes

In reviewing the literature, we found no liver cell carcinoma (LCC) or well-documented adult polycystic kidneys (APK) associated with congenital hepatic fibrosis (CHF). We report a 69-year-old man with CHF, LCC, APK, duplication cyst of distal portion of stomach, two calcified splenic artery aneurysms, myocardial fibrosis and muscular hypertrophy of esophagus. The LCC was grossly predunculated and microscopically showed prominent fibrosis and hyaline intracytoplasmic inclusions in the tumor cells.

UI MeSH Term Description Entries
D007690 Polycystic Kidney Diseases Hereditary diseases that are characterized by the progressive expansion of a large number of tightly packed CYSTS within the KIDNEYS. They include diseases with autosomal dominant and autosomal recessive inheritance. Kidney, Polycystic,Polycystic Kidney,Polycystic Kidney Disease,Polycystic Kidneys,Polycystic Renal Disease,Disease, Polycystic Kidney,Disease, Polycystic Renal,Diseases, Polycystic Kidney,Diseases, Polycystic Renal,Kidney Disease, Polycystic,Kidney Diseases, Polycystic,Kidneys, Polycystic,Polycystic Renal Diseases,Renal Disease, Polycystic,Renal Diseases, Polycystic
D008107 Liver Diseases Pathological processes of the LIVER. Liver Dysfunction,Disease, Liver,Diseases, Liver,Dysfunction, Liver,Dysfunctions, Liver,Liver Disease,Liver Dysfunctions
D008113 Liver Neoplasms Tumors or cancer of the LIVER. Cancer of Liver,Hepatic Cancer,Liver Cancer,Cancer of the Liver,Cancer, Hepatocellular,Hepatic Neoplasms,Hepatocellular Cancer,Neoplasms, Hepatic,Neoplasms, Liver,Cancer, Hepatic,Cancer, Liver,Cancers, Hepatic,Cancers, Hepatocellular,Cancers, Liver,Hepatic Cancers,Hepatic Neoplasm,Hepatocellular Cancers,Liver Cancers,Liver Neoplasm,Neoplasm, Hepatic,Neoplasm, Liver
D008297 Male Males
D006528 Carcinoma, Hepatocellular A primary malignant neoplasm of epithelial liver cells. It ranges from a well-differentiated tumor with EPITHELIAL CELLS indistinguishable from normal HEPATOCYTES to a poorly differentiated neoplasm. The cells may be uniform or markedly pleomorphic, or form GIANT CELLS. Several classification schemes have been suggested. Hepatocellular Carcinoma,Hepatoma,Liver Cancer, Adult,Liver Cell Carcinoma,Liver Cell Carcinoma, Adult,Adult Liver Cancer,Adult Liver Cancers,Cancer, Adult Liver,Cancers, Adult Liver,Carcinoma, Liver Cell,Carcinomas, Hepatocellular,Carcinomas, Liver Cell,Cell Carcinoma, Liver,Cell Carcinomas, Liver,Hepatocellular Carcinomas,Hepatomas,Liver Cancers, Adult,Liver Cell Carcinomas
D006801 Humans Members of the species Homo sapiens. Homo sapiens,Man (Taxonomy),Human,Man, Modern,Modern Man
D000368 Aged A person 65 years of age or older. For a person older than 79 years, AGED, 80 AND OVER is available. Elderly

Related Publications

J L Manes, and J M Kissane, and A J Valdes
Congenital fibrosis and polycystic disease of liver and kidneys.
September 1973, American journal of diseases of children (1960),
J L Manes, and J M Kissane, and A J Valdes
Congenital hepatic fibrosis with polycystic disease of the kidneys.
December 1982, Hepato-gastroenterology,
J L Manes, and J M Kissane, and A J Valdes
Kidney polycystic disease in adult congenital hepatic fibrosis.
April 1978, Annals of internal medicine,
J L Manes, and J M Kissane, and A J Valdes
[Coexistent congenital polycystic kidneys and liver].
July 1986, Wiadomosci lekarskie (Warsaw, Poland : 1960),
J L Manes, and J M Kissane, and A J Valdes
Infantile polycystic disease of the kidneys and liver: clinical, pathological and radiological correlations and comparison with congenital hepatic fibrosis.
July 1971, Medicine,
J L Manes, and J M Kissane, and A J Valdes
Congenital hepatic fibrosis with saccular dilatation of intrahepatic bile ducts and infantile polycystic kidneys.
January 1986, Pediatric radiology,
J L Manes, and J M Kissane, and A J Valdes
[Congenital hepatic fibrosis and polycystic disease of the kidneys in two siblings (author's transl)].
May 1977, Klinische Padiatrie,
J L Manes, and J M Kissane, and A J Valdes
Neonatal diabetes mellitus, congenital hypothyroidism, hepatic fibrosis, polycystic kidneys, and congenital glaucoma: a new autosomal recessive syndrome?
October 2003, American journal of medical genetics. Part A,
J L Manes, and J M Kissane, and A J Valdes
WEEKLY clinicopathological exercises: congenital polycystic kidneys and liver.
March 1952, The New England journal of medicine,
J L Manes, and J M Kissane, and A J Valdes
Congenital Polycystic Disease of the Liver and Kidneys.
April 1946, British medical journal,
Copied contents to your clipboard!