BACKGROUND Mammary-type myofibroblastomas have been reported at extramammary sites, especially along the mammary midline, but not previously in the vulva. METHODS A 56-year-old woman presented with complaints of a left vulvar mass, pelvic organ prolapse and urinary incontinence. Examination revealed a 3-cm,firm vulvar mass, located in close proximity to the Bartholin's gland. CONCLUSIONS Although myofibroblastomas have been reported at extramammary sites, this is this first reported case in the vulva. These masses are densely adherent to surrounding tissue, which can lead to a difficult dissection. Therefore they should be removed in the operating room with appropriate equipment and sedation.