Congenital pulmonary fibrosarcoma in a newborn with hypoglycemia and respiratory distress: case report. 2010

Davut Sahin, and Nermin Koç, and Seref Etker, and Sirin Güven, and Cengiz Canpolat
Department of Pathology, Zeynep-Kamil Gynecology and Pediatrics Training and Research Hospital, Istanbul, Turkey.

Although primary bronchopulmonary fibrosarcoma is a rare tumor, it may be characterized by the symptoms of acute respiratory distress occurring during the first moments of life in a newborn. It is one of the leading congenital malignant neoplasms of the lung, but is considered a borderline tumor since its biological behavior is much more favorable than that of adult fibrosarcomas. In the absence of metastases, complete resection is curative. Histopathological diagnosis is not simple, as the microscopic characteristics may be confused with benign fibromatosis or malignant mesenchymal neoplasms. In this case report, we present a case of congenital pulmonary spindle cell tumor showing the features of fibrosarcoma, and we discuss the differential diagnosis of spindle cell lesions localized within the thorax.

UI MeSH Term Description Entries
D007003 Hypoglycemia A syndrome of abnormally low BLOOD GLUCOSE level. Clinical hypoglycemia has diverse etiologies. Severe hypoglycemia eventually lead to glucose deprivation of the CENTRAL NERVOUS SYSTEM resulting in HUNGER; SWEATING; PARESTHESIA; impaired mental function; SEIZURES; COMA; and even DEATH. Fasting Hypoglycemia,Postabsorptive Hypoglycemia,Postprandial Hypoglycemia,Reactive Hypoglycemia,Hypoglycemia, Fasting,Hypoglycemia, Postabsorptive,Hypoglycemia, Postprandial,Hypoglycemia, Reactive
D007231 Infant, Newborn An infant during the first 28 days after birth. Neonate,Newborns,Infants, Newborn,Neonates,Newborn,Newborn Infant,Newborn Infants
D008175 Lung Neoplasms Tumors or cancer of the LUNG. Cancer of Lung,Lung Cancer,Pulmonary Cancer,Pulmonary Neoplasms,Cancer of the Lung,Neoplasms, Lung,Neoplasms, Pulmonary,Cancer, Lung,Cancer, Pulmonary,Cancers, Lung,Cancers, Pulmonary,Lung Cancers,Lung Neoplasm,Neoplasm, Lung,Neoplasm, Pulmonary,Pulmonary Cancers,Pulmonary Neoplasm
D012131 Respiratory Insufficiency Failure to adequately provide oxygen to cells of the body and to remove excess carbon dioxide from them. (Stedman, 25th ed) Acute Hypercapnic Respiratory Failure,Acute Hypoxemic Respiratory Failure,Hypercapnic Acute Respiratory Failure,Hypercapnic Respiratory Failure,Hypoxemic Acute Respiratory Failure,Hypoxemic Respiratory Failure,Respiratory Depression,Respiratory Failure,Ventilatory Depression,Depressions, Ventilatory,Failure, Hypercapnic Respiratory,Failure, Hypoxemic Respiratory,Failure, Respiratory,Hypercapnic Respiratory Failures,Hypoxemic Respiratory Failures,Respiratory Failure, Hypercapnic,Respiratory Failure, Hypoxemic,Respiratory Failures
D005354 Fibrosarcoma A sarcoma derived from deep fibrous tissue, characterized by bundles of immature proliferating fibroblasts with variable collagen formation, which tends to invade locally and metastasize by the bloodstream. (Stedman, 25th ed) Fibrosarcomas
D006801 Humans Members of the species Homo sapiens. Homo sapiens,Man (Taxonomy),Human,Man, Modern,Modern Man

Related Publications

Davut Sahin, and Nermin Koç, and Seref Etker, and Sirin Güven, and Cengiz Canpolat
June 2023, Journal francais d'ophtalmologie,
Davut Sahin, and Nermin Koç, and Seref Etker, and Sirin Güven, and Cengiz Canpolat
February 2017, Clinical chemistry,
Davut Sahin, and Nermin Koç, and Seref Etker, and Sirin Güven, and Cengiz Canpolat
May 1951, A.M.A. archives of pathology,
Davut Sahin, and Nermin Koç, and Seref Etker, and Sirin Güven, and Cengiz Canpolat
January 2018, Wiadomosci lekarskie (Warsaw, Poland : 1960),
Davut Sahin, and Nermin Koç, and Seref Etker, and Sirin Güven, and Cengiz Canpolat
January 2016, Respiration; international review of thoracic diseases,
Davut Sahin, and Nermin Koç, and Seref Etker, and Sirin Güven, and Cengiz Canpolat
October 1978, South Dakota journal of medicine,
Davut Sahin, and Nermin Koç, and Seref Etker, and Sirin Güven, and Cengiz Canpolat
May 1995, The Journal of reproductive medicine,
Davut Sahin, and Nermin Koç, and Seref Etker, and Sirin Güven, and Cengiz Canpolat
January 1997, Medical and pediatric oncology,
Davut Sahin, and Nermin Koç, and Seref Etker, and Sirin Güven, and Cengiz Canpolat
September 1979, AJR. American journal of roentgenology,
Davut Sahin, and Nermin Koç, and Seref Etker, and Sirin Güven, and Cengiz Canpolat
March 2024, Clinical pediatrics,
Copied contents to your clipboard!