This work is devoted to the haemodynamic pathogenesis of congenital vascular-bone syndromes. It is based on our studies of 209 patients suffering from angio-osteohypertrophic and angio-osteohypotrophic syndromes as regards the species and anatomopathological forms of the vascular defects, the haemodynamics, tissue metabolism and changes in the tubular bones. Establishing the haemodynamic pathogenesis of congenital vascular-bone syndromes in vascular defects is very important in determining the principles of their surgical treatment. It offers the possibility of a correct choice of operative tactics and techniques in these severe vascular diseases, which in many cases lead to disability and cardiovascular insufficiency.