The paper reports on a clinical case of association between pigmentary retinopathy and Coat's retinal vasculopathy. The study of the clinical syndrome of the case presented and of those described in the literature, shows the possibility that vascular telangiecstases might be the consequence of a hereditary tendency towards a form of latent vasculopathy, that develops towards a known clinical form. The disturbances of a generalized retinal vascular permeability, described for the first time in this context seems to be dependent on the genetic type of pigmentary retinopathy and independent of the peripheral telangiectatic modifications. The association of the two affections is, by the serious complications they generate, a factor of aggravating the visual prognosis.