Conduction velocity along muscle fibers in situ in Duchenne muscular dystrophy. 1990

A Cruz Martinez, and J M Lopez Terradas
Section of Electromyography, Hospital La Paz, Madrid, Spain.

The muscle fibers of the biceps brachii muscle were stimulated distally with low voltage by means of two monopolar needles in 14 boys with Duchenne muscular dystrophy (DD). The electric activity was recorded proximally by means of a SFEMG electrode. The mean conduction velocity of 508 muscle fibers in situ (MFCV) calculated with this method shows that MFCV in DD patients (2.38 +/- .94 m/sec) is significantly slower than in 20 control children of the same age (3.24 +/- .53 m/sec). The distribution frequency of MFCV in all fibers tested in healthy children shows a Gaussian distribution (mode = 3.2 m/sec). In DD patients the distribution frequency is bimodal with spikes at 1.2 and 2.4 m/sec. Significant decrease in minimum propagation velocity and increased SD values were other striking results in patients with DD. Slowing and large variation in MFCV were significantly correlated with some findings in a coaxial needle electromyogram, such as long polyphasics and motor unit potentials followed by satellites. Satellites might arise from atrophic muscle fibers with slow conduction velocity. The results of MFCV were supported by the pathologic findings in DD subjects. The reported method for MFCV in situ is reliable and easy to apply in children, has merit for testing the size and function of muscle fiber, and helps to explain some electropathologic features in DD patients.

UI MeSH Term Description Entries
D008297 Male Males
D009136 Muscular Dystrophies A heterogeneous group of inherited MYOPATHIES, characterized by wasting and weakness of the SKELETAL MUSCLE. They are categorized by the sites of MUSCLE WEAKNESS; AGE OF ONSET; and INHERITANCE PATTERNS. Muscular Dystrophy,Myodystrophica,Myodystrophy,Dystrophies, Muscular,Dystrophy, Muscular,Myodystrophicas,Myodystrophies
D009435 Synaptic Transmission The communication from a NEURON to a target (neuron, muscle, or secretory cell) across a SYNAPSE. In chemical synaptic transmission, the presynaptic neuron releases a NEUROTRANSMITTER that diffuses across the synaptic cleft and binds to specific synaptic receptors, activating them. The activated receptors modulate specific ion channels and/or second-messenger systems in the postsynaptic cell. In electrical synaptic transmission, electrical signals are communicated as an ionic current flow across ELECTRICAL SYNAPSES. Neural Transmission,Neurotransmission,Transmission, Neural,Transmission, Synaptic
D009469 Neuromuscular Junction The synapse between a neuron and a muscle. Myoneural Junction,Nerve-Muscle Preparation,Junction, Myoneural,Junction, Neuromuscular,Junctions, Myoneural,Junctions, Neuromuscular,Myoneural Junctions,Nerve Muscle Preparation,Nerve-Muscle Preparations,Neuromuscular Junctions,Preparation, Nerve-Muscle,Preparations, Nerve-Muscle
D002648 Child A person 6 to 12 years of age. An individual 2 to 5 years old is CHILD, PRESCHOOL. Children
D002675 Child, Preschool A child between the ages of 2 and 5. Children, Preschool,Preschool Child,Preschool Children
D004558 Electric Stimulation Use of electric potential or currents to elicit biological responses. Stimulation, Electric,Electrical Stimulation,Electric Stimulations,Electrical Stimulations,Stimulation, Electrical,Stimulations, Electric,Stimulations, Electrical
D004576 Electromyography Recording of the changes in electric potential of muscle by means of surface or needle electrodes. Electromyogram,Surface Electromyography,Electromyograms,Electromyographies,Electromyographies, Surface,Electromyography, Surface,Surface Electromyographies
D004594 Electrophysiology The study of the generation and behavior of electrical charges in living organisms particularly the nervous system and the effects of electricity on living organisms.
D006801 Humans Members of the species Homo sapiens. Homo sapiens,Man (Taxonomy),Human,Man, Modern,Modern Man

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