| D016878 |
POEMS Syndrome |
A multisystemic disorder characterized by a sensorimotor polyneuropathy (POLYNEUROPATHIES), organomegaly, endocrinopathy, monoclonal gammopathy, and pigmentary skin changes. Other clinical features which may be present include EDEMA; CACHEXIA; microangiopathic glomerulopathy; pulmonary hypertension (HYPERTENSION, PULMONARY); cutaneous necrosis; THROMBOCYTOSIS; and POLYCYTHEMIA. This disorder is frequently associated with osteosclerotic myeloma. (From Adams et al., Principles of Neurology, 6th ed, p1335; Rev Med Interne 1997;18(7):553-62) |
Crow-Fukase Syndrome,Takatsuki's Syndrome,Polyneuropathy Organomegaly,Polyneuropathy, Organomegaly, Endocrinopathy, M Protein, and Skin Changes Syndrome,Crow Fukase Syndrome,Organomegalies, Polyneuropathy,Organomegaly, Polyneuropathy,Polyneuropathy Organomegalies,Syndrome, Crow-Fukase,Syndrome, POEMS,Syndrome, Takatsuki's,Takatsuki Syndrome |
|