BIOMAT Database Logo BIOMAT Database Logo

Aortic root reimplantation for isolated sinus of valsalva aneurysm in the patient with Marfan's syndrome. 2012

Keitaro Nakagiri, and Tasuku Kadowaki, and Naoto Morimoto, and Hirohisa Murakami, and Masato Yoshida, and Nobuhiko Mukohara
Department of Cardiovascular Surgery, Hyogo Brain and Heart Center at Himeji, Himeji, Japan. knakagiri@hbhc.jp

We describe an isolated extracardiac unruptured acquired aneurysm in the right coronary sinus of Valsalva, which was seen in a 55-year-old woman with Marfan's syndrome. The patient underwent aortic root replacement using a reimplantation technique. Pathologic examination revealed absence of the medial elastic fiber of the aortic wall of the normal sinus of Valsalva. This result supports the preference of entire root replacement instead of patch repair of the affected sinus for the isolated aneurysm in 1 sinus of Valsalva in a patient with Marfan's syndrome.

UI MeSH Term Description Entries
D008382 Marfan Syndrome An autosomal dominant disorder of CONNECTIVE TISSUE with abnormal features in the heart, the eye, and the skeleton. Cardiovascular manifestations include MITRAL VALVE PROLAPSE; AORTIC ANEURYSM; and AORTIC DISSECTION. Other features include lens displacement (ectopia lentis), disproportioned long limbs and enlarged DURA MATER (dural ectasia). Marfan syndrome (type 1) is associated with mutations in the gene encoding FIBRILLIN-1 (FBN1), a major element of extracellular microfibrils of connective tissue. Mutations in the gene encoding TYPE II TGF-BETA RECEPTOR (TGFBR2) are associated with Marfan syndrome type 2. Marfan Like Connective Tissue Disorder,Marfan Syndrome Type 1,Marfan Syndrome Type 2,Marfan Syndrome, Type II,Marfan Syndrome, Type I,Marfan's Syndrome,Marfans Syndrome
D008875 Middle Aged An adult aged 45 - 64 years. Middle Age
D005260 Female Females
D006348 Cardiac Surgical Procedures Surgery performed on the heart. Cardiac Surgical Procedure,Heart Surgical Procedure,Heart Surgical Procedures,Procedure, Cardiac Surgical,Procedure, Heart Surgical,Procedures, Cardiac Surgical,Procedures, Heart Surgical,Surgical Procedure, Cardiac,Surgical Procedure, Heart,Surgical Procedures, Cardiac,Surgical Procedures, Heart
D006801 Humans Members of the species Homo sapiens. Homo sapiens,Man (Taxonomy),Human,Man, Modern,Modern Man
D001014 Aortic Aneurysm An abnormal balloon- or sac-like dilatation in the wall of AORTA. Aneurysm, Aortic,Aneurysms, Aortic,Aortic Aneurysms
D001021 Aortic Valve The valve between the left ventricle and the ascending aorta which prevents backflow into the left ventricle. Aortic Valves,Valve, Aortic,Valves, Aortic
D012850 Sinus of Valsalva The dilatation of the aortic wall behind each of the cusps of the aortic valve. Aortic Sinus,Sinus, Aortic,Valsalva Sinus

Related Publications

Keitaro Nakagiri, and Tasuku Kadowaki, and Naoto Morimoto, and Hirohisa Murakami, and Masato Yoshida, and Nobuhiko Mukohara
[Aortic Root Reimplantation for Extra-cardiac Unruptured Sinus of Valsalva Aneurysm].
April 2015, Kyobu geka. The Japanese journal of thoracic surgery,
Keitaro Nakagiri, and Tasuku Kadowaki, and Naoto Morimoto, and Hirohisa Murakami, and Masato Yoshida, and Nobuhiko Mukohara
Repair of isolated, symptomatic, sinus of Valsalva aneurysm in a patient with Marfan's syndrome.
January 1988, The Canadian journal of cardiology,
Keitaro Nakagiri, and Tasuku Kadowaki, and Naoto Morimoto, and Hirohisa Murakami, and Masato Yoshida, and Nobuhiko Mukohara
Aortic root replacement for Valsalva sinus aneurysm with lupus erythematosus.
April 2012, Asian cardiovascular & thoracic annals,
Keitaro Nakagiri, and Tasuku Kadowaki, and Naoto Morimoto, and Hirohisa Murakami, and Masato Yoshida, and Nobuhiko Mukohara
Giant Aortic Root Aneurysm in Marfan's Syndrome.
March 2021, The Journal of invasive cardiology,
Keitaro Nakagiri, and Tasuku Kadowaki, and Naoto Morimoto, and Hirohisa Murakami, and Masato Yoshida, and Nobuhiko Mukohara
Root repair in patient with huge sinus Valsalva aneurysm and severe aortic regurgitation.
May 2020, General thoracic and cardiovascular surgery,
Keitaro Nakagiri, and Tasuku Kadowaki, and Naoto Morimoto, and Hirohisa Murakami, and Masato Yoshida, and Nobuhiko Mukohara
[Rupture of the aneurysm of the sinus of Valsalva in Marfan's syndrome].
December 1981, Klinicheskaia meditsina,
Keitaro Nakagiri, and Tasuku Kadowaki, and Naoto Morimoto, and Hirohisa Murakami, and Masato Yoshida, and Nobuhiko Mukohara
Partial aortic root replacement for aneurysm of the right sinus of Valsalva.
June 2015, Asian cardiovascular & thoracic annals,
Keitaro Nakagiri, and Tasuku Kadowaki, and Naoto Morimoto, and Hirohisa Murakami, and Masato Yoshida, and Nobuhiko Mukohara
Isolated descending thoracic aortic aneurysm in Marfan's syndrome.
May 1988, The American journal of cardiology,
Keitaro Nakagiri, and Tasuku Kadowaki, and Naoto Morimoto, and Hirohisa Murakami, and Masato Yoshida, and Nobuhiko Mukohara
Aortic Root Abscess in a Patient with Marfan's Syndrome.
June 2019, The American journal of medicine,
Keitaro Nakagiri, and Tasuku Kadowaki, and Naoto Morimoto, and Hirohisa Murakami, and Masato Yoshida, and Nobuhiko Mukohara
Rare Presentation of Sinus of Valsalva Aneurysm Treated by Aortic Valve Reimplantation Technique.
December 2022, Brazilian journal of cardiovascular surgery,
Copied contents to your clipboard!