Angioimmunoblastic T-cell lymphoma-associated pure red cell aplasia with abdominal pain. 2013

Jin Tao, and Feng-Ping Zheng, and Hong Tian, and Ying Lin, and Jian-Zhong Li, and Xiao-Liang Chen, and Jian-Ning Chen, and Chun-Kui Shao, and Bin Wu
Jin Tao, Feng-Ping Zheng, Hong Tian, Ying Lin, Jian-Zhong Li, Xiao-Liang Chen, Bin Wu, Department of Gastroenterology, The Third Affiliated Hospital of Sun Yat-Sen University, Guangzhou 510630, Guangdong Province, China.

Angioimmunoblastic T-cell lymphoma (AITL) is a unique type of peripheral T-cell lymphoma with a constellation of clinical symptoms and signs, including weight loss, fever, chills, anemia, skin rash, hepatosplenomegaly, lymphadenopathy, thrombocytopenia and polyclonal hypergammaglobulinemia. The histological features of AITL are also distinctive. Pure red cell aplasia is a bone marrow failure characterized by progressive normocytic anemia and reticulocytopenia without leucopenia or thrombocytopenia. However, AITL with abdominal pain and pure red cell aplasia has rarely been reported. Here, we report a rare case of AITL-associated pure red cell aplasia with abdominal pain. The diagnosis was verified by a biopsy of the enlarged abdominal lymph nodes with immunohistochemical staining.

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