Orbital alveolar soft part sarcoma: Histopathologic report of two cases. 2010

Hind Alkatan, and Ahlam A Al-Shedoukhy, and Imtiaz A Chaudhry, and Ayman Al-Ayoubi
Department of Pathology and Laboratory Medicine, King Khaled Eye Specialist Hospital, Riyadh, Saudi Arabia.

Alveolar soft part sarcoma is considered as a distinct histopathological entity with rare cases reported from the orbit area. Two cases of alveolar soft part sarcomas occurring in the orbit of two patients along with their histopathologic findings are reported herewith. In both cases, the patients presented with eyelid swelling and proptosis. The diagnosis was made by incisional biopsies and histopathology. The literature is reviewed regarding occurrence of this tumor, its diagnosis and management.

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