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We report a 5-month-old Sudanese boy with a probable diagnosis of Congenital Nephrotic Syndrome. Our case had features which are neither typical of the Finnish type nor of other hereditary renal diseases. Histologically, the most striking changes were in the glomerular basement membranes which show patchy thinning, thick segments (with reduplication) and occasional low spikes. Tubules are well preserved, and no foam cells were seen. Electron microscopy showed extensive fusion of foot processes with podocyte microvilli. In parts the glomerular basement membrane shows irregular thickening and splitting, and incorporation of podocyte cytoplasm into the membrane. In other areas there is marked thinning of the basement membrane. Immunological features include a high level of IgA and IgG. To our knowledge such features have not been described before.
E M Elshibly, and
M Z Mohammed, and
M O Elrab, and
A R Morley, and
S M Suliman, and
E M Elmelik, and
B I Mukhtar
January 1963,
Annales paediatriae Fenniae,
E M Elshibly, and
M Z Mohammed, and
M O Elrab, and
A R Morley, and
S M Suliman, and
E M Elmelik, and
B I Mukhtar
January 1967,
Acta paediatrica Scandinavica,
E M Elshibly, and
M Z Mohammed, and
M O Elrab, and
A R Morley, and
S M Suliman, and
E M Elmelik, and
B I Mukhtar
December 1986,
The Journal of communicable diseases,
E M Elshibly, and
M Z Mohammed, and
M O Elrab, and
A R Morley, and
S M Suliman, and
E M Elmelik, and
B I Mukhtar
January 1964,
Revista espanola de pediatria,
E M Elshibly, and
M Z Mohammed, and
M O Elrab, and
A R Morley, and
S M Suliman, and
E M Elmelik, and
B I Mukhtar
May 1967,
Journal of clinical pathology,
E M Elshibly, and
M Z Mohammed, and
M O Elrab, and
A R Morley, and
S M Suliman, and
E M Elmelik, and
B I Mukhtar
March 1967,
Journal of clinical pathology,
E M Elshibly, and
M Z Mohammed, and
M O Elrab, and
A R Morley, and
S M Suliman, and
E M Elmelik, and
B I Mukhtar
January 2019,
Journal of biological regulators and homeostatic agents,
E M Elshibly, and
M Z Mohammed, and
M O Elrab, and
A R Morley, and
S M Suliman, and
E M Elmelik, and
B I Mukhtar
July 1991,
Pediatric nephrology (Berlin, Germany),
E M Elshibly, and
M Z Mohammed, and
M O Elrab, and
A R Morley, and
S M Suliman, and
E M Elmelik, and
B I Mukhtar
February 1980,
Annals of tropical medicine and parasitology,
E M Elshibly, and
M Z Mohammed, and
M O Elrab, and
A R Morley, and
S M Suliman, and
E M Elmelik, and
B I Mukhtar
August 2016,
Pediatric nephrology (Berlin, Germany),
