Case for diagnosis. Dermatofibrosarcoma protuberans. 2014

Joanna Pimenta de Araujo Franco, and Caroline Cruz Barbosa, and Bárbara Ferreira Saraiva da Fonseca, and Ricardo Barbosa Lima, and Antônio Macedo D'Acri, and Carlos José Martins
State of Rio de Janeiro Federal University, Rio de Janeiro, RJ, Brazil.

Dermatofibrosarcoma protuberans is a fibrohistiocytic tumor of intermediate malignancy with aggressive localized growth, high recurrence rate, but low metastatic potential. It appears as a hardened plaque, with slow growth, upon which the development of nodules occurs. It predominates in the trunk and is unusual in acral locations. Histopathology reveals spindle cells with storiform pattern and cartwheel-like or whirlwind-like aspect. Immunohistochemistry shows positivity for CD34. The treatment is surgical. We report a case of long evolution, with an unusual location, that relapsed after surgery, to emphasize the importance of early diagnosis and proper treatment, avoiding aggressive resections with increased morbidity.

UI MeSH Term Description Entries
D007150 Immunohistochemistry Histochemical localization of immunoreactive substances using labeled antibodies as reagents. Immunocytochemistry,Immunogold Techniques,Immunogold-Silver Techniques,Immunohistocytochemistry,Immunolabeling Techniques,Immunogold Technics,Immunogold-Silver Technics,Immunolabeling Technics,Immunogold Silver Technics,Immunogold Silver Techniques,Immunogold Technic,Immunogold Technique,Immunogold-Silver Technic,Immunogold-Silver Technique,Immunolabeling Technic,Immunolabeling Technique,Technic, Immunogold,Technic, Immunogold-Silver,Technic, Immunolabeling,Technics, Immunogold,Technics, Immunogold-Silver,Technics, Immunolabeling,Technique, Immunogold,Technique, Immunogold-Silver,Technique, Immunolabeling,Techniques, Immunogold,Techniques, Immunogold-Silver,Techniques, Immunolabeling
D008875 Middle Aged An adult aged 45 - 64 years. Middle Age
D005260 Female Females
D005385 Fingers Four or five slender jointed digits in humans and primates, attached to each HAND. Finger
D006801 Humans Members of the species Homo sapiens. Homo sapiens,Man (Taxonomy),Human,Man, Modern,Modern Man
D001706 Biopsy Removal and pathologic examination of specimens from the living body. Biopsies
D012878 Skin Neoplasms Tumors or cancer of the SKIN. Cancer of Skin,Skin Cancer,Cancer of the Skin,Neoplasms, Skin,Cancer, Skin,Cancers, Skin,Neoplasm, Skin,Skin Cancers,Skin Neoplasm
D016896 Treatment Outcome Evaluation undertaken to assess the results or consequences of management and procedures used in combating disease in order to determine the efficacy, effectiveness, safety, and practicability of these interventions in individual cases or series. Rehabilitation Outcome,Treatment Effectiveness,Clinical Effectiveness,Clinical Efficacy,Patient-Relevant Outcome,Treatment Efficacy,Effectiveness, Clinical,Effectiveness, Treatment,Efficacy, Clinical,Efficacy, Treatment,Outcome, Patient-Relevant,Outcome, Rehabilitation,Outcome, Treatment,Outcomes, Patient-Relevant,Patient Relevant Outcome,Patient-Relevant Outcomes
D018223 Dermatofibrosarcoma A sarcoma of the deep layers of the skin. The tumors are locally aggressive tends to recur but rarely metastatic. It can be classified into variants depending on the cell type tumors are derived from or by its characteristics: Pigmented variant from MELANIN-containing DERMAL DENDRITIC CELLS; Myxoid variant, myxoid STROMAL CELLS; Giant cell variant characterized by GIANT CELLS in the tumors; and Fibrosarcomatous variant chracterized by tumor areas histologically indistinguishable from FIBROSARCOMA. Bednar Tumor,Bednar's Tumor,DFSP, Fibrosarcomatous,DFSP, Juvenile,DFSP, Myxoid,DFSP, Pigmented,Darier-Ferrand Tumor,Darier-Hoffmann Tumor,Dermatofibrosarcoma Protuberan,Dermatofibrosarcoma Protuberans, Familial,Dermatofibrosarcoma Protuberans, Fibrosarcomatous,Dermatofibrosarcoma Protuberans, Giant Cell,Dermatofibrosarcoma Protuberans, Myxoid,Dermatofibrosarcoma Protuberans, Pigmented,FS-DFSP,Familial Dermatofibrosarcoma Protuberans,Fibrosarcomatous Dermatofibrosarcoma Protuberans,Giant Cell Fibroblastoma,Giant Dermatofibrosarcoma Protuberans,Metastatic Dermatofibrosarcoma Protuberans,Bednars Tumor,Cell Fibroblastoma, Giant,Cell Fibroblastomas, Giant,DFSPs, Fibrosarcomatous,DFSPs, Juvenile,DFSPs, Myxoid,DFSPs, Pigmented,Darier Ferrand Tumor,Darier Hoffmann Tumor,Dermatofibrosarcoma Protuberan, Familial,Dermatofibrosarcoma Protuberan, Fibrosarcomatous,Dermatofibrosarcoma Protuberan, Giant,Dermatofibrosarcoma Protuberan, Metastatic,Dermatofibrosarcoma Protuberan, Myxoid,Dermatofibrosarcoma Protuberan, Pigmented,Dermatofibrosarcoma Protuberans,Dermatofibrosarcoma Protuberans, Giant,Dermatofibrosarcoma Protuberans, Metastatic,Dermatofibrosarcomas,Familial Dermatofibrosarcoma Protuberan,Fibroblastoma, Giant Cell,Fibroblastomas, Giant Cell,Fibrosarcomatous DFSP,Fibrosarcomatous DFSPs,Fibrosarcomatous Dermatofibrosarcoma Protuberan,Giant Cell Fibroblastomas,Giant Dermatofibrosarcoma Protuberan,Juvenile DFSP,Juvenile DFSPs,Metastatic Dermatofibrosarcoma Protuberan,Myxoid DFSP,Myxoid DFSPs,Myxoid Dermatofibrosarcoma Protuberan,Myxoid Dermatofibrosarcoma Protuberans,Pigmented DFSP,Pigmented DFSPs,Pigmented Dermatofibrosarcoma Protuberan,Pigmented Dermatofibrosarcoma Protuberans,Protuberan, Dermatofibrosarcoma,Protuberan, Familial Dermatofibrosarcoma,Protuberan, Fibrosarcomatous Dermatofibrosarcoma,Protuberan, Giant Dermatofibrosarcoma,Protuberan, Metastatic Dermatofibrosarcoma,Protuberan, Myxoid Dermatofibrosarcoma,Protuberan, Pigmented Dermatofibrosarcoma,Protuberans, Dermatofibrosarcoma,Protuberans, Familial Dermatofibrosarcoma,Protuberans, Fibrosarcomatous Dermatofibrosarcoma,Protuberans, Giant Dermatofibrosarcoma,Protuberans, Metastatic Dermatofibrosarcoma,Protuberans, Myxoid Dermatofibrosarcoma,Protuberans, Pigmented Dermatofibrosarcoma,Tumor, Bednar,Tumor, Bednar's,Tumor, Darier-Ferrand,Tumor, Darier-Hoffmann

Related Publications

Joanna Pimenta de Araujo Franco, and Caroline Cruz Barbosa, and Bárbara Ferreira Saraiva da Fonseca, and Ricardo Barbosa Lima, and Antônio Macedo D'Acri, and Carlos José Martins
January 2010, Anais brasileiros de dermatologia,
Joanna Pimenta de Araujo Franco, and Caroline Cruz Barbosa, and Bárbara Ferreira Saraiva da Fonseca, and Ricardo Barbosa Lima, and Antônio Macedo D'Acri, and Carlos José Martins
January 1982, Scandinavian journal of plastic and reconstructive surgery,
Joanna Pimenta de Araujo Franco, and Caroline Cruz Barbosa, and Bárbara Ferreira Saraiva da Fonseca, and Ricardo Barbosa Lima, and Antônio Macedo D'Acri, and Carlos José Martins
January 1999, Medicinski pregled,
Joanna Pimenta de Araujo Franco, and Caroline Cruz Barbosa, and Bárbara Ferreira Saraiva da Fonseca, and Ricardo Barbosa Lima, and Antônio Macedo D'Acri, and Carlos José Martins
August 1969, Seikeigeka. Orthopedic surgery,
Joanna Pimenta de Araujo Franco, and Caroline Cruz Barbosa, and Bárbara Ferreira Saraiva da Fonseca, and Ricardo Barbosa Lima, and Antônio Macedo D'Acri, and Carlos José Martins
March 1983, Wiadomosci lekarskie (Warsaw, Poland : 1960),
Joanna Pimenta de Araujo Franco, and Caroline Cruz Barbosa, and Bárbara Ferreira Saraiva da Fonseca, and Ricardo Barbosa Lima, and Antônio Macedo D'Acri, and Carlos José Martins
July 1974, Zeitschrift fur Hautkrankheiten,
Joanna Pimenta de Araujo Franco, and Caroline Cruz Barbosa, and Bárbara Ferreira Saraiva da Fonseca, and Ricardo Barbosa Lima, and Antônio Macedo D'Acri, and Carlos José Martins
May 2005, Diagnostic cytopathology,
Joanna Pimenta de Araujo Franco, and Caroline Cruz Barbosa, and Bárbara Ferreira Saraiva da Fonseca, and Ricardo Barbosa Lima, and Antônio Macedo D'Acri, and Carlos José Martins
September 2021, Photodiagnosis and photodynamic therapy,
Joanna Pimenta de Araujo Franco, and Caroline Cruz Barbosa, and Bárbara Ferreira Saraiva da Fonseca, and Ricardo Barbosa Lima, and Antônio Macedo D'Acri, and Carlos José Martins
April 1958, Dermatologische Wochenschrift,
Joanna Pimenta de Araujo Franco, and Caroline Cruz Barbosa, and Bárbara Ferreira Saraiva da Fonseca, and Ricardo Barbosa Lima, and Antônio Macedo D'Acri, and Carlos José Martins
October 1955, British journal of plastic surgery,
Copied contents to your clipboard!