BIOMAT Database Logo BIOMAT Database Logo

Keratoconus in Alagille's syndrome. 1989

E I Traboulsi, and J M Lustbader, and M A Lemp
Center for Sight, Georgetown University Medical Center, Washington, DC 20007.

UI MeSH Term Description Entries
D007640 Keratoconus A noninflammatory, usually bilateral protrusion and thinning of the CORNEA, the apex being displaced downward and nasally. It occurs most commonly in females at about puberty. Two closely related noninflammatory corneal ectasias are pellucid marginal degeneration and keratoglobus. Keratoglobus,Pellucid Marginal Corneal Degeneration,Pellucid Marginal Degeneration,Degeneration, Pellucid Marginal,Marginal Degeneration, Pellucid,Pellucid Marginal Degenerations
D011666 Pulmonary Valve Stenosis The pathologic narrowing of the orifice of the PULMONARY VALVE. This lesion restricts blood outflow from the RIGHT VENTRICLE to the PULMONARY ARTERY. When the trileaflet valve is fused into an imperforate membrane, the blockage is complete. Pulmonary Stenosis,Pulmonary Stenoses,Pulmonary Valve Stenoses,Pulmonic Stenosis,Stenoses, Pulmonary,Stenoses, Pulmonary Valve,Stenosis, Pulmonary,Stenosis, Pulmonary Valve,Valvular Pulmonic Stenosis,Pulmonary Stenose,Pulmonic Stenoses,Pulmonic Stenoses, Valvular,Pulmonic Stenosis, Valvular,Stenose, Pulmonary,Stenoses, Pulmonic,Stenosis, Pulmonic,Valvular Pulmonic Stenoses
D002779 Cholestasis Impairment of bile flow due to obstruction in small bile ducts (INTRAHEPATIC CHOLESTASIS) or obstruction in large bile ducts (EXTRAHEPATIC CHOLESTASIS). Bile Duct Obstruction,Biliary Stasis,Bile Duct Obstructions,Biliary Stases,Cholestases,Duct Obstruction, Bile,Duct Obstructions, Bile,Obstruction, Bile Duct,Obstructions, Bile Duct,Stases, Biliary,Stasis, Biliary
D005260 Female Females
D006499 Hepatic Artery A branch of the celiac artery that distributes to the stomach, pancreas, duodenum, liver, gallbladder, and greater omentum. Arteries, Hepatic,Artery, Hepatic,Hepatic Arteries
D006801 Humans Members of the species Homo sapiens. Homo sapiens,Man (Taxonomy),Human,Man, Modern,Modern Man
D000328 Adult A person having attained full growth or maturity. Adults are of 19 through 44 years of age. For a person between 19 and 24 years of age, YOUNG ADULT is available. Adults
D001653 Bile Ducts, Intrahepatic Passages within the liver for the conveyance of bile. Includes right and left hepatic ducts even though these may join outside the liver to form the common hepatic duct. Bile Duct, Intrahepatic,Duct, Intrahepatic Bile,Ducts, Intrahepatic Bile,Intrahepatic Bile Duct,Intrahepatic Bile Ducts
D013577 Syndrome A characteristic symptom complex. Symptom Cluster,Cluster, Symptom,Clusters, Symptom,Symptom Clusters,Syndromes

Related Publications

E I Traboulsi, and J M Lustbader, and M A Lemp
Renal histopathology in Alagille's syndrome.
January 1987, Pediatric pathology,
E I Traboulsi, and J M Lustbader, and M A Lemp
[Ocular anomalies in Alagille's syndrome].
January 1991, Journal francais d'ophtalmologie,
E I Traboulsi, and J M Lustbader, and M A Lemp
Lymphatic abnormalities in Alagille's syndrome.
March 1991, British heart journal,
E I Traboulsi, and J M Lustbader, and M A Lemp
Alagille's syndrome. New manifestations.
February 1996, Clinical nuclear medicine,
E I Traboulsi, and J M Lustbader, and M A Lemp
[Alagille's syndrome: variable expressivity].
October 1988, Archives francaises de pediatrie,
E I Traboulsi, and J M Lustbader, and M A Lemp
Nephropathy in arteriohepatic dysplasia (Alagille's syndrome).
January 1988, Child nephrology and urology,
E I Traboulsi, and J M Lustbader, and M A Lemp
Xanthomatous biliary cirrhosis in Alagille's syndrome.
April 1988, Journal of the American Academy of Dermatology,
E I Traboulsi, and J M Lustbader, and M A Lemp
Liver transplantation for Alagille's syndrome.
March 1993, Archives of surgery (Chicago, Ill. : 1960),
E I Traboulsi, and J M Lustbader, and M A Lemp
Variation in liver histology in Alagille's syndrome.
June 1981, The American journal of gastroenterology,
E I Traboulsi, and J M Lustbader, and M A Lemp
[Intrahepatic portal venous hypoplasia in Alagille's syndrome].
February 1985, Archives francaises de pediatrie,
Copied contents to your clipboard!