Biomaterial Database

Fibrofolliculomas, tricodiscomas and acrochordons (Birt-Hogg-Dubé) associated with intestinal polyposis. 1989

F Rongioletti, and R Hazini, and G Gianotti, and A Rebora

We describe a patient with multiple fibrofolliculomas (FF), tricodiscomas (TD) and acrochordons (Birt-Hogg-Dubé) associated with intestinal polyps. One of the polyps presented histological features of marked dysplasia. This association may not be fortuitous and suggests that patients with multiple hamartomas of the perifollicular connective tissue should be examined periodically for intestinal polyps before malignancy develops.

UI	MeSH Term	Description	Entries
D008297	Male		Males
D008875	Middle Aged	An adult aged 45 - 64 years.	Middle Age
D009378	Neoplasms, Multiple Primary	Two or more abnormal growths of tissue occurring simultaneously and presumed to be of separate origin. The neoplasms may be histologically the same or different, and may be found in the same or different sites.	Neoplasms, Synchronous,Neoplasms, Synchronous Multiple Primary,Multiple Primary Neoplasms,Multiple Primary Neoplasms, Synchronous,Synchronous Multiple Primary Neoplasms,Synchronous Neoplasms,Multiple Primary Neoplasm,Neoplasm, Multiple Primary,Neoplasm, Synchronous,Primary Neoplasm, Multiple,Primary Neoplasms, Multiple,Synchronous Neoplasm
D003111	Colonic Polyps	Discrete tissue masses that protrude into the lumen of the COLON. These POLYPS are connected to the wall of the colon either by a stalk, pedunculus, or by a broad base.	Colonic Polyp,Polyp, Colonic,Polyps, Colonic
D006223	Hamartoma Syndrome, Multiple	A hereditary disease characterized by multiple ectodermal, mesodermal, and endodermal nevoid and neoplastic anomalies. Facial trichilemmomas and papillomatous papules of the oral mucosa are the most characteristic lesions. Individuals with this syndrome have a high risk of BREAST CANCER; THYROID CANCER; and ENDOMETRIAL CANCER. This syndrome is associated with mutations in the gene for PTEN PHOSPHATASE.	Bannayan-Riley-Ruvalcaba Syndrome,Cowden Disease,Cowden's Disease,Lhermitte-Duclos Disease,Multiple Hamartoma Syndrome,PTEN Hamartoma Tumor Syndrome,Bannayan-Ruvalcaba-Riley Syndrome,Bannayan-Zonana Syndrome,Cowden Syndrome,Cowden's Syndrome,Dysplastic Gangliocytoma of Cerebellum,Dysplastic Gangliocytoma of the Cerebellum,Macrocephaly, Multiple Lipomas, and Hemangiomata,Macrocephaly, Pseudopapilledema, and Multiple Hemangiomas,Macrocephaly, Pseudopapilledema, and Multiple Hemangiomata,Myhre-Riley-Smith Syndrome,Riley-Smith Syndrome,Ruvalcaba-Myhre Syndrome,Ruvalcaba-Myhre-Smith Syndrome,Bannayan Riley Ruvalcaba Syndrome,Bannayan Zonana Syndrome,Cerebellum Dysplastic Gangliocytoma,Cerebellum Dysplastic Gangliocytomas,Cowdens Disease,Cowdens Syndrome,Hamartoma Syndromes, Multiple,Lhermitte Duclos Disease,Multiple Hamartoma Syndromes,Myhre Riley Smith Syndrome,Riley Smith Syndrome,Ruvalcaba Myhre Smith Syndrome
D006801	Humans	Members of the species Homo sapiens.	Homo sapiens,Man (Taxonomy),Human,Man, Modern,Modern Man
D000236	Adenoma	A benign epithelial tumor with a glandular organization.	Adenoma, Basal Cell,Adenoma, Follicular,Adenoma, Microcystic,Adenoma, Monomorphic,Adenoma, Papillary,Adenoma, Trabecular,Adenomas,Adenomas, Basal Cell,Adenomas, Follicular,Adenomas, Microcystic,Adenomas, Monomorphic,Adenomas, Papillary,Adenomas, Trabecular,Basal Cell Adenoma,Basal Cell Adenomas,Follicular Adenoma,Follicular Adenomas,Microcystic Adenoma,Microcystic Adenomas,Monomorphic Adenoma,Monomorphic Adenomas,Papillary Adenoma,Papillary Adenomas,Trabecular Adenoma,Trabecular Adenomas
D012867	Skin	The outer covering of the body that protects it from the environment. It is composed of the DERMIS and the EPIDERMIS.
D012878	Skin Neoplasms	Tumors or cancer of the SKIN.	Cancer of Skin,Skin Cancer,Cancer of the Skin,Neoplasms, Skin,Cancer, Skin,Cancers, Skin,Neoplasm, Skin,Skin Cancers,Skin Neoplasm