Gardner's syndrome is an association of rectopolyposis, to which the prognosis is related, with bony lesions : osteomas, essentially craniofacial, and osteocementosis : dental : multiple inclusions, supernumerary teeth; and cutaneous manifestations : lipomas, adenomas, fibromas ; and sometimes desmoid tumours, either cutaneous at the site of an abdominal scar, sometimes mesenteric. This complex histodysplasia, subject to the possibility of complications where it occurs (in particular craniofacial osteomas) requires digestive surveillance and further treatment when necessary : colectomy with colo-rectal anastomosis associated with coagulation diathermy of rectal polyps. When the latter is impossible, abdominoperineal excision of the rectum is followed by permanent ileostomy.