Moyamoya disease is a vascular form of neurocristopathy: disease of the embryologic cephalic neural crest. 2017

Masaki Komiyama
Department of Neuro-Intervention, Osaka City General Hospital, Osaka, Japan. komiyama@japan-mail.com.

UI MeSH Term Description Entries
D009072 Moyamoya Disease A noninflammatory, progressive occlusion of the intracranial CAROTID ARTERIES and the formation of netlike collateral arteries arising from the CIRCLE OF WILLIS. Cerebral angiogram shows the puff-of-smoke (moyamoya) collaterals at the base of the brain. It is characterized by endothelial HYPERPLASIA and FIBROSIS with thickening of arterial walls. This disease primarily affects children but can also occur in adults. Cerebrovascular Moyamoya Disease,Progressive Intracranial Occlusive Arteropathy (Moyamoya),Moya-Moya Disease,Moyamoya Disease, Classic,Moyamoya Disease, Primary,Moyamoya Disease, Secondary,Moyamoya Syndrome,Classic Moyamoya Disease,Disease, Classic Moyamoya,Disease, Moya-Moya,Disease, Primary Moyamoya,Moya Moya Disease,Moyamoya Diseases, Primary,Primary Moyamoya Disease,Primary Moyamoya Diseases,Secondary Moyamoya Disease
D009432 Neural Crest The two longitudinal ridges along the PRIMITIVE STREAK appearing near the end of GASTRULATION during development of nervous system (NEURULATION). The ridges are formed by folding of NEURAL PLATE. Between the ridges is a neural groove which deepens as the fold become elevated. When the folds meet at midline, the groove becomes a closed tube, the NEURAL TUBE. Neural Crest Cells,Neural Fold,Neural Groove,Cell, Neural Crest,Cells, Neural Crest,Crest, Neural,Crests, Neural,Fold, Neural,Folds, Neural,Groove, Neural,Grooves, Neural,Neural Crest Cell,Neural Crests,Neural Folds,Neural Grooves
D006801 Humans Members of the species Homo sapiens. Homo sapiens,Man (Taxonomy),Human,Man, Modern,Modern Man
D000015 Abnormalities, Multiple Congenital abnormalities that affect more than one organ or body structure. Multiple Abnormalities

Related Publications

Masaki Komiyama
January 1979, Advances in anatomy, embryology, and cell biology,
Masaki Komiyama
August 1999, Development (Cambridge, England),
Masaki Komiyama
January 1981, Acta oto-laryngologica,
Masaki Komiyama
May 1991, Development (Cambridge, England),
Masaki Komiyama
September 2009, Proceedings of the National Academy of Sciences of the United States of America,
Masaki Komiyama
January 2024, Journal of clinical imaging science,
Masaki Komiyama
March 1996, Development (Cambridge, England),
Copied contents to your clipboard!