Takayasu's arteritis presenting as pulmonary hypertension. 1986

A Haas, and E R Stiehm

Takayasu's arteritis (pulseless disease) is a vasculitis that affects the large arteries, including the aorta, its branches, and the pulmonary arteries. A 15-year-old girl with Takayasu's arteritis was referred to our institution for marked pulmonary hypertension in the absence of symptoms referable to systemic vasculitis. She was shown to have a thickened, narrowed thoracic aorta, a stenosed right axillary artery, and severely affected pulmonary arteries. Despite corticosteroid therapy she died one month after diagnosis. This patient's illness indicates that pulmonary vessels might be the principal vessels involved in Takayasu's arteritis.

UI MeSH Term Description Entries
D006976 Hypertension, Pulmonary Increased VASCULAR RESISTANCE in the PULMONARY CIRCULATION, usually secondary to HEART DISEASES or LUNG DISEASES. Pulmonary Hypertension
D011651 Pulmonary Artery The short wide vessel arising from the conus arteriosus of the right ventricle and conveying unaerated blood to the lungs. Arteries, Pulmonary,Artery, Pulmonary,Pulmonary Arteries
D003937 Diagnosis, Differential Determination of which one of two or more diseases or conditions a patient is suffering from by systematically comparing and contrasting results of diagnostic measures. Diagnoses, Differential,Differential Diagnoses,Differential Diagnosis
D005260 Female Females
D006801 Humans Members of the species Homo sapiens. Homo sapiens,Man (Taxonomy),Human,Man, Modern,Modern Man
D000293 Adolescent A person 13 to 18 years of age. Adolescence,Youth,Adolescents,Adolescents, Female,Adolescents, Male,Teenagers,Teens,Adolescent, Female,Adolescent, Male,Female Adolescent,Female Adolescents,Male Adolescent,Male Adolescents,Teen,Teenager,Youths
D001015 Aortic Arch Syndromes Conditions resulting from abnormalities in the arteries branching from the ASCENDING AORTA, the curved portion of the aorta. These syndromes are results of occlusion or abnormal blood flow to the head-neck or arm region leading to neurological defects and weakness in an arm. These syndromes are associated with vascular malformations; ATHEROSCLEROSIS; TRAUMA; and blood clots. Aortic Arch Syndrome,Syndrome, Aortic Arch,Syndromes, Aortic Arch
D001167 Arteritis INFLAMMATION of any ARTERIES. Arterial Inflammation,Arteritides,Inflammation, Arterial
D013625 Takayasu Arteritis A chronic inflammatory process that affects the AORTA and its primary branches, such as the brachiocephalic artery (BRACHIOCEPHALIC TRUNK) and CAROTID ARTERIES. It results in progressive arterial stenosis, occlusion, and aneurysm formation. The pulse in the arm is hard to detect. Patients with aortitis syndrome often exhibit retinopathy. Aortitis Syndrome,Arteritis, Takayasu's,Pulseless Disease,Takayasu Disease,Takayasu Syndrome,Takayasu's Arteritis,Young Female Arteritis,Arteritides, Young Female,Arteritis, Takayasu,Arteritis, Takayasus,Arteritis, Young Female,Disease, Takayasu,Female Arteritides, Young,Female Arteritis, Young,Syndrome, Aortitis,Takayasus Arteritis,Young Female Arteritides

Related Publications

A Haas, and E R Stiehm
March 2013, Saudi journal of kidney diseases and transplantation : an official publication of the Saudi Center for Organ Transplantation, Saudi Arabia,
A Haas, and E R Stiehm
December 1974, Australian and New Zealand journal of medicine,
A Haas, and E R Stiehm
April 2007, Clinical rheumatology,
A Haas, and E R Stiehm
December 2023, The Journal of invasive cardiology,
A Haas, and E R Stiehm
December 2015, Pediatrics and neonatology,
A Haas, and E R Stiehm
January 1997, Texas Heart Institute journal,
A Haas, and E R Stiehm
April 2022, Current problems in cardiology,
A Haas, and E R Stiehm
February 1976, Angiology,
A Haas, and E R Stiehm
December 2001, Journal of clinical rheumatology : practical reports on rheumatic & musculoskeletal diseases,
A Haas, and E R Stiehm
June 2002, JPMA. The Journal of the Pakistan Medical Association,
Copied contents to your clipboard!