Bullous pemphigoid accompanied by IgA nephropathy and atypical haemolytic uraemic syndrome. 2018

Kazumasa Oya, and Rei Watanabe, and Sae Inoue, and Naoshi Obara, and Yusuke Kiyoki, and Mamiko Sakata-Yanagimoto, and Shigeru Chiba, and Chie Saito, and Yutaka Matsumura, and Yoshiyuki Nakamura, and Yosuke Ishitsuka, and Hiroshi Maruyama, and Naoko Okiyama, and Yasuhiro Fujisawa, and Manabu Fujimoto
Department of Dermatology.

UI MeSH Term Description Entries
D010391 Pemphigoid, Bullous A chronic and relatively benign subepidermal blistering disease usually of the elderly and without histopathologic acantholysis. Pemphigoid,Bullous Pemphigoid,Pemphigoids
D005260 Female Females
D005922 Glomerulonephritis, IGA A chronic form of glomerulonephritis characterized by deposits of predominantly IMMUNOGLOBULIN A in the mesangial area (GLOMERULAR MESANGIUM). Deposits of COMPLEMENT C3 and IMMUNOGLOBULIN G are also often found. Clinical features may progress from asymptomatic HEMATURIA to END-STAGE KIDNEY DISEASE. Berger Disease,Immunoglobulin A Nephropathy,Nephropathy, IGA,Berger's Disease,IGA Glomerulonephritis,IGA Nephropathy,Iga Nephropathy 1,Nephritis, IGA Type,Bergers Disease,Glomerulonephritides, IGA,IGA Type Nephritis,Nephropathy 1, Iga,Nephropathy, Immunoglobulin A
D006801 Humans Members of the species Homo sapiens. Homo sapiens,Man (Taxonomy),Human,Man, Modern,Modern Man
D000328 Adult A person having attained full growth or maturity. Adults are of 19 through 44 years of age. For a person between 19 and 24 years of age, YOUNG ADULT is available. Adults
D065766 Atypical Hemolytic Uremic Syndrome An hereditary hemolytic uremic syndrome associated with variations in the gene that encodes COMPLEMENT FACTOR H, or the related proteins CFHR1 and CFHR3. Disease often progresses to CHRONIC KIDNEY FAILURE without the prodromal symptoms of ENTEROCOLITIS and DIARRHEA that characterize typical hemolytic uremic syndrome. Atypical Hemolytic-Uremic Syndrome,Hemolytic Uremic Syndrome, Atypical,Non-Shiga-Like Toxin-Associated HUS,Non-Stx-Hus,Nonenteropathic HUS,Atypical Hemolytic-Uremic Syndromes,HUS, Non-Shiga-Like Toxin-Associated,HUS, Nonenteropathic,HUSs, Non-Shiga-Like Toxin-Associated,HUSs, Nonenteropathic,Hemolytic-Uremic Syndrome, Atypical,Hemolytic-Uremic Syndromes, Atypical,Non Shiga Like Toxin Associated HUS,Non Stx Hus,Non-Shiga-Like Toxin-Associated HUSs,Nonenteropathic HUSs,Syndrome, Atypical Hemolytic-Uremic,Syndromes, Atypical Hemolytic-Uremic,Toxin-Associated HUS, Non-Shiga-Like,Toxin-Associated HUSs, Non-Shiga-Like

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