Imaging assessment of profound sensorineural deafness with inner ear anatomical abnormalities. 2015

Wei-Jing Wu, and Xiang-Bo He, and Li-Hua Tan, and Peng Hu, and An-Quan Peng, and Zi-An Xiao, and Shu Yang, and Tian Wang, and Jie Qing, and Xin Chen, and Jing-Kun Li, and Tao Peng, and Yun-Peng Dong, and Xue-Zhong Liu, and Ding-Hua Xie
Department of Otolaryngology and Head & Neck Surgery, Institute of Otology, Second Xiangya Hospital, Central South University, Changsha, Hunan, 410011, China.

OBJECTIVE To explore the value of a combined computed tomography (CT) and magnetic resonance imaging (MRI) in evaluating profound sensorineural deafness patients before cochlear implant (CI) surgery. METHODS A retrospective analysis of 1012 cases of profound sensorineural deafness that received CI was performed. RESULTS A total of 96 cases were diagnosed with inner ear abnormalities including large vestibular aqueduct syndrome (LVAS, n = 61), Michel deformity (n = 3), cochlear incomplete partition I (n = 2), cochlear incomplete partition II (n = 6), cochlear hypoplasia with vestibular malformation (n = 3), cochlear ossification (n = 3), bilateral internal auditory canal obstruction (n = 5) and internal auditory canal stenosis (n = 2). CONCLUSIONS High resolution CT (HRCT) can display bony structures while MRI can image the membranous labyrinth in preoperative evaluation for cochlear implantation. The combination of these two modalities provides reliable anatomical information regarding the bony and membranous labyrinths, as well as the auditory nerve.

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