Cystic fibrosis disease severity correlates with plasma levels of desmosine and isodesmosine, biomarkers of elastin degradation. 2019

Shuren Ma, and Patrick Geraghty, and Abdoulaye Dabo, and Cormac McCarthy, and N Gerry McElvaney, and Gerard M Turino
Dept of Medicine, Mount Sinai St Luke's Hospital, New York, NY, USA.

Novel methodological approaches now demonstrate that the unique elastin degradation products desmosine and isodesmosine are detectable in plasma of cystic fibrosis patients and correlate to lung function, exacerbation frequency and disease progression http://bit.ly/2VwZOcx.

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