Prenatal Diagnosis and Immediate Successful Management of Isolated Fetal Epignathus. 2019

Mohamed ElSherbiny Hamed, and Mohamed Hassan Naser El-Din, and Ibrahim A Abdelazim, and Svetlana Shikanova, and Bakyt Karimova, and Sakiyeva Kanshaiym
Department of Obstetrics and Gynecology, Ain Shams University, Cairo, Egypt.

Epignathus or enigmatic teratoma is rare congenital tumor, arising from the sphenoid region of the palate or pharynx. A 30-year-old pregnant woman presented at 34 weeks + 2 days' gestation with a well-defined solid mass measuring 6.47 cm × 5.7 cm arising from the fetal oral cavity. The color flow mapping showed that the mass was well vascularized, especially in its center, and its blood supply was originated from the fetal oral cavity. The newborn has no chromosomal abnormalities or other associated anomalies and/or intracranial extension immediately and successfully managed after delivery to highlight the importance of prenatal diagnosis and the importance of multidisciplinary team management.

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