BIOMAT Database Logo BIOMAT Database Logo

Endobronchial pulmonary blastoma - an unusual presentation of a rare lung malignancy and review of literature. 2020

Benhur Joel Shadrach, and Deepak Vedant, and Vikarn Vishwajeet, and Priyank Jain, and Naveen Dutt, and Binit Surekha, and Puneet Pareek, and Poonam Abhay Elhence
Department of Pulmonary Medicine, All India Institute of Medical Sciences, Jodhpur. benjoe6326@gmail.com.

Biphasic pulmonary blastoma (BPB) is an extremely rare highly aggressive malignant tumor that arises from fetal lung tissue and has the classical biphasic histology of epithelial and mesenchymal components. It is usually seen in adults with a slight male predominance and smokers. Previously grouped along with well-differentiated fetal adenocarcinoma (WDFA), and pleuropulmonary blastoma (PPB), now it is considered a separate variant and grouped under sarcomatoid neoplasms. Symptoms include chest pain, cough, hemoptysis and it is asymptomatic in at least one-third of the cases. A biopsy is essential for diagnosis and surgical excision is the treatment of choice. Prognosis is poor with 5-year survival less than 20% and recurrence occurring within 12 months of surgery. An aggressive multimodality approach is required for its management and active follow up surveillance is needed to look for recurrence.

UI MeSH Term Description Entries
D008175 Lung Neoplasms Tumors or cancer of the LUNG. Cancer of Lung,Lung Cancer,Pulmonary Cancer,Pulmonary Neoplasms,Cancer of the Lung,Neoplasms, Lung,Neoplasms, Pulmonary,Cancer, Lung,Cancer, Pulmonary,Cancers, Lung,Cancers, Pulmonary,Lung Cancers,Lung Neoplasm,Neoplasm, Lung,Neoplasm, Pulmonary,Pulmonary Cancers,Pulmonary Neoplasm
D008297 Male Males
D009367 Neoplasm Staging Methods which attempt to express in replicable terms the extent of the neoplasm in the patient. Cancer Staging,Staging, Neoplasm,Tumor Staging,TNM Classification,TNM Staging,TNM Staging System,Classification, TNM,Classifications, TNM,Staging System, TNM,Staging Systems, TNM,Staging, Cancer,Staging, TNM,Staging, Tumor,System, TNM Staging,Systems, TNM Staging,TNM Classifications,TNM Staging Systems
D001999 Bronchoscopy Endoscopic examination, therapy or surgery of the bronchi. Bronchoscopic Surgical Procedures,Surgical Procedures, Bronchoscopic,Bronchoscopic Surgery,Surgery, Bronchoscopic,Bronchoscopic Surgeries,Bronchoscopic Surgical Procedure,Bronchoscopies,Surgeries, Bronchoscopic,Surgical Procedure, Bronchoscopic
D002637 Chest Pain Pressure, burning, or numbness in the chest. Precordial Catch,Precordial Catch Syndrome,Texidor's Twinge,Chest Pains,Pain, Chest,Pains, Chest,Syndrome, Precordial Catch,Texidor Twinge
D003371 Cough A sudden, audible expulsion of air from the lungs through a partially closed glottis, preceded by inhalation. It is a protective response that serves to clear the trachea, bronchi, and/or lungs of irritants and secretions, or to prevent aspiration of foreign materials into the lungs. Coughs
D006469 Hemoptysis Expectoration or spitting of blood originating from any part of the RESPIRATORY TRACT, usually from hemorrhage in the lung parenchyma (PULMONARY ALVEOLI) and the BRONCHIAL ARTERIES. Hemoptyses
D006801 Humans Members of the species Homo sapiens. Homo sapiens,Man (Taxonomy),Human,Man, Modern,Modern Man
D000072078 Positron Emission Tomography Computed Tomography An imaging technique that combines a POSITRON-EMISSION TOMOGRAPHY (PET) scanner and a CT X RAY scanner. This establishes a precise anatomic localization in the same session. CT PET,CT PET Scan,PET CT Scan,PET-CT,PET-CT Scan,Positron Emission Tomography-Computed Tomography,CT PET Scans,CT Scan, PET,CT Scans, PET,PET CT Scans,PET Scan, CT,PET Scans, CT,PET-CT Scans,Scan, CT PET,Scan, PET CT,Scan, PET-CT,Scans, CT PET,Scans, PET CT,Scans, PET-CT
D000328 Adult A person having attained full growth or maturity. Adults are of 19 through 44 years of age. For a person between 19 and 24 years of age, YOUNG ADULT is available. Adults

Related Publications

Benhur Joel Shadrach, and Deepak Vedant, and Vikarn Vishwajeet, and Priyank Jain, and Naveen Dutt, and Binit Surekha, and Puneet Pareek, and Poonam Abhay Elhence
Pulmonary blastoma: a rare lung malignancy.
September 1996, Lung cancer (Amsterdam, Netherlands),
Benhur Joel Shadrach, and Deepak Vedant, and Vikarn Vishwajeet, and Priyank Jain, and Naveen Dutt, and Binit Surekha, and Puneet Pareek, and Poonam Abhay Elhence
Pulmonary blastoma: a rare primary lung malignancy.
January 2012, Case reports in medicine,
Benhur Joel Shadrach, and Deepak Vedant, and Vikarn Vishwajeet, and Priyank Jain, and Naveen Dutt, and Binit Surekha, and Puneet Pareek, and Poonam Abhay Elhence
An Unusual and Rare Presentation of Pulmonary Aspergillosis: Endobronchial Aspergilloma.
January 2021, Case reports in infectious diseases,
Benhur Joel Shadrach, and Deepak Vedant, and Vikarn Vishwajeet, and Priyank Jain, and Naveen Dutt, and Binit Surekha, and Puneet Pareek, and Poonam Abhay Elhence
Pulmonary blastoma: a rare childhood malignancy.
June 1991, Radiology,
Benhur Joel Shadrach, and Deepak Vedant, and Vikarn Vishwajeet, and Priyank Jain, and Naveen Dutt, and Binit Surekha, and Puneet Pareek, and Poonam Abhay Elhence
A rare presentation of biphasic pulmonary blastoma.
July 2002, Archives of pathology & laboratory medicine,
Benhur Joel Shadrach, and Deepak Vedant, and Vikarn Vishwajeet, and Priyank Jain, and Naveen Dutt, and Binit Surekha, and Puneet Pareek, and Poonam Abhay Elhence
Pulmonary blastoma: a rare case of childhood malignancy.
January 1992, Pediatric radiology,
Benhur Joel Shadrach, and Deepak Vedant, and Vikarn Vishwajeet, and Priyank Jain, and Naveen Dutt, and Binit Surekha, and Puneet Pareek, and Poonam Abhay Elhence
Classic biphasic pulmonary blastoma (CBPB): a rare primary pulmonary malignancy.
August 2021, BMJ case reports,
Benhur Joel Shadrach, and Deepak Vedant, and Vikarn Vishwajeet, and Priyank Jain, and Naveen Dutt, and Binit Surekha, and Puneet Pareek, and Poonam Abhay Elhence
[Blastoma of the lung--a rare malignancy. Case report].
September 1993, Helvetica chirurgica acta,
Benhur Joel Shadrach, and Deepak Vedant, and Vikarn Vishwajeet, and Priyank Jain, and Naveen Dutt, and Binit Surekha, and Puneet Pareek, and Poonam Abhay Elhence
Endobronchial aspergilloma: An unusual presentation of pulmonary aspergillosis.
January 2016, Revista portuguesa de pneumologia,
Benhur Joel Shadrach, and Deepak Vedant, and Vikarn Vishwajeet, and Priyank Jain, and Naveen Dutt, and Binit Surekha, and Puneet Pareek, and Poonam Abhay Elhence
Pulmonary blastoma--a rare tumor with variable presentation.
February 2006, European journal of cardio-thoracic surgery : official journal of the European Association for Cardio-thoracic Surgery,
Copied contents to your clipboard!