Biomaterial Database

Norwood-I in a hypoplastic left heart variant and right aortic arch. 2021

Antonio Amodeo, and Martin Schweiger, and Tugba Erdil, and Michael Hübler

Children's Heart Centre, University Children's Hospital, Zurich, Switzerland.

Even though preoperative diagnostics have improved significantly, intraoperative surprises may still occur especially in the case of complex congenital heart disease. An instance of such a complex congenital heart disease is a hypoplastic left heart syndrome with a right-sided aortic arch. In this case report, we present 1 patient with such a complex and unexpected anatomy, as well as a possible way to overcome the obstacles.

UI	MeSH Term	Description	Entries
D006801	Humans	Members of the species Homo sapiens.	Homo sapiens,Man (Taxonomy),Human,Man, Modern,Modern Man
D001013	Aorta, Thoracic	The portion of the descending aorta proceeding from the arch of the aorta and extending to the DIAPHRAGM, eventually connecting to the ABDOMINAL AORTA.	Aorta, Ascending,Aorta, Descending,Aortic Arch,Aortic Root,Arch of the Aorta,Descending Aorta,Sinotubular Junction,Ascending Aorta,Thoracic Aorta,Aortic Roots,Arch, Aortic,Ascending Aortas,Junction, Sinotubular,Root, Aortic,Sinotubular Junctions
D012857	Situs Inversus	A congenital abnormality in which organs in the THORAX and the ABDOMEN are opposite to their normal positions (situs solitus) due to lateral transposition. Normally the STOMACH and SPLEEN are on the left, LIVER on the right, the three-lobed right lung is on the right, and the two-lobed left lung on the left. Situs inversus has a familial pattern and has been associated with a number of genes related to microtubule-associated proteins.	Situs Inversus Viscerum,Inversus, Situs
D018636	Hypoplastic Left Heart Syndrome	A condition caused by underdevelopment of the whole left half of the heart. It is characterized by hypoplasia of the left cardiac chambers (HEART ATRIUM; HEART VENTRICLE), the AORTA, the AORTIC VALVE, and the MITRAL VALVE. Severe symptoms appear in early infancy when DUCTUS ARTERIOSUS closes.	Left Heart Syndrome, Hypoplastic,Left Heart Hypoplasia Syndrome