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Hepatobiliary fibropolycystic diseases. Two cases of Caroli's disease. 1987

J Teufel, and U M Farack
Dept. of Gastroenterology, Kreiskrankenhaus Pfaffenhofen, FRG.

Two case reports of Caroli's disease type I are given. The main clinical features were recurrent severe cholangitis, biliary colics, and persistent cholestasis. Both cases demonstrate the predominance in males and the prevalence of symptoms in adults up to the sixth decade. No features of congenital hepatic fibrosis or biliary cirrhosis and no renal pathomorphological changes could be detected. Investigations of their family members did not reveal genetic aspects.

UI MeSH Term Description Entries
D008297 Male Males
D008875 Middle Aged An adult aged 45 - 64 years. Middle Age
D002761 Cholangitis Inflammation of the biliary ductal system (BILE DUCTS); intrahepatic, extrahepatic, or both. Cholangitides
D003560 Cysts Any fluid-filled closed cavity or sac that is lined by an EPITHELIUM. Cysts can be of normal, abnormal, non-neoplastic, or neoplastic tissues. Cyst
D006801 Humans Members of the species Homo sapiens. Homo sapiens,Man (Taxonomy),Human,Man, Modern,Modern Man
D001649 Bile Duct Diseases Diseases in any part of the ductal system of the BILIARY TRACT from the smallest BILE CANALICULI to the largest COMMON BILE DUCT. Bile Duct Disease,Disease, Bile Duct,Diseases, Bile Duct,Duct Disease, Bile,Duct Diseases, Bile

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