We made the subject's review of the connective naevus because a boy of thirteen years old has consulted us about it. He has it on the back, on the forearm and on the right, it is associated to a cavernous tubero angioma of the mouth, this eventuality was described and commented by McBurney and his coworkers (1979) in his article "Angiokeratomas, connective tissue nevus, hemangioma". We bring out its main characteristics based on publications and displays of national authors' cases and our experience achieved at the cathedra about this nevoid dysplasia, from universal rareness, motif that will help to increase the scarce statistics of associate connective tissue naevus.