Cysticercosis is caused by parasitic infestation mainly by the larval form of Taenia solium. Orbital cysticercosis may involve both the intraocular structures and orbit particularly the extraocular muscles. The clinical manifestations are caused mainly by the mass effect of the cyst in the initial period resulting in ocular motility restriction and proptosis and depends primarily on the site of the lesion. Here we report a case of 27 years old male with orbital apex syndrome secondary to myocysticercosis. Orbital myocysticercosis often mimics various eye pathologies like as isolated nerve palsy, orbital pseudotumor, orbital cellulitis. Acute vision loss in a case of orbital cysticerosis is mainly due to compressive optic neuropathy due to cystic lesion of extra ocular muscle or by direct invasion of the optic nerve. In our case, MRI orbit revealed cysticercosis of lateral rectus at orbital apex where it compressed the optic nerve resulting compressive optic neuropathy. Albendazole along with steroid was used as the first-line treatment. This case highlights that Orbital Apex Syndrome Secondary to Myocysticercosis is a rare and can lead to severe visual loss if not managed timely.