Angioimmunoblastic lymphadenopathy with dysproteinaemia (AILD) and sicca syndrome. 1986

Y J Bignon, and A Janin-Mercier, and J J Dubost, and J M Ristori, and Y Fonck, and J C Alphonse, and B J Sauvezie

We report a case of AILD and sicca syndrome. The patient had presented with renal insufficiency, lymphadenopathy, hepatosplenomegaly, polyclonal hypergammaglobulinaemia, dryness of the eyes and mouth. Lip biopsy specimens showed an unusual cellular infiltrate similar to his kidney lesions. Data from the eight previously reported cases support the hypothesis that the association is a distinct pathological entity differing from pseudolymphoma and malignant lymphoma, which occur in the course of Sjögren's syndrome. The recognition of AILD is important because lymphoproliferation may lead to death after a few months.

UI MeSH Term Description Entries
D007119 Immunoblastic Lymphadenopathy A disorder characterized by proliferation of arborizing small vessels, prominent immunoblastic proliferations and amorphous acidophilic interstitial material. Clinical manifestations include fever, sweats, weight loss, generalized lymphadenopathy and frequently hepatosplenomegaly. Angioimmunoblastic Lymphadenopathy,Lymphadenopathy, Immunoblastic,Angioimmunoblastic Lymphadenopathies,Immunoblastic Lymphadenopathies,Lymphadenopathies, Angioimmunoblastic,Lymphadenopathies, Immunoblastic,Lymphadenopathy, Angioimmunoblastic
D008297 Male Males
D010265 Paraproteinemias A group of related diseases characterized by an unbalanced or disproportionate proliferation of immunoglobulin-producing cells, usually from a single clone. These cells frequently secrete a structurally homogeneous immunoglobulin (M-component) and/or an abnormal immunoglobulin. Gammapathy, Monoclonal,Gammopathy, Monoclonal,Monoclonal Gammopathies,Paraimmunoglobulinemia,Paraimmunoglobulinemias,Paraproteinemia,Plasma Cell Dyscrasias,Monoclonal Gammapathies,Monoclonal Gammopathy,Cell Dyscrasia, Plasma,Dyscrasia, Plasma Cell,Monoclonal Gammapathy,Plasma Cell Dyscrasia
D006801 Humans Members of the species Homo sapiens. Homo sapiens,Man (Taxonomy),Human,Man, Modern,Modern Man
D000368 Aged A person 65 years of age or older. For a person older than 79 years, AGED, 80 AND OVER is available. Elderly
D012859 Sjogren's Syndrome Chronic inflammatory and autoimmune disease in which the salivary and lacrimal glands undergo progressive destruction by lymphocytes and plasma cells resulting in decreased production of saliva and tears. The primary form, often called sicca syndrome, involves both KERATOCONJUNCTIVITIS SICCA and XEROSTOMIA. The secondary form includes, in addition, the presence of a connective tissue disease, usually rheumatoid arthritis. Sicca Syndrome,Sjogren Syndrome,Sjogrens Syndrome,Syndrome, Sicca,Syndrome, Sjogren's

Related Publications

Y J Bignon, and A Janin-Mercier, and J J Dubost, and J M Ristori, and Y Fonck, and J C Alphonse, and B J Sauvezie
October 1989, The Journal of the Association of Physicians of India,
Y J Bignon, and A Janin-Mercier, and J J Dubost, and J M Ristori, and Y Fonck, and J C Alphonse, and B J Sauvezie
April 1987, The Journal of the Association of Physicians of India,
Y J Bignon, and A Janin-Mercier, and J J Dubost, and J M Ristori, and Y Fonck, and J C Alphonse, and B J Sauvezie
January 1996, Haematologia,
Y J Bignon, and A Janin-Mercier, and J J Dubost, and J M Ristori, and Y Fonck, and J C Alphonse, and B J Sauvezie
December 1994, Archives of dermatology,
Y J Bignon, and A Janin-Mercier, and J J Dubost, and J M Ristori, and Y Fonck, and J C Alphonse, and B J Sauvezie
April 1979, Journal of clinical pathology,
Y J Bignon, and A Janin-Mercier, and J J Dubost, and J M Ristori, and Y Fonck, and J C Alphonse, and B J Sauvezie
June 1979, Journal of neurology, neurosurgery, and psychiatry,
Y J Bignon, and A Janin-Mercier, and J J Dubost, and J M Ristori, and Y Fonck, and J C Alphonse, and B J Sauvezie
January 1992, Verhandlungen der Deutschen Gesellschaft fur Pathologie,
Y J Bignon, and A Janin-Mercier, and J J Dubost, and J M Ristori, and Y Fonck, and J C Alphonse, and B J Sauvezie
January 2005, Respirology (Carlton, Vic.),
Y J Bignon, and A Janin-Mercier, and J J Dubost, and J M Ristori, and Y Fonck, and J C Alphonse, and B J Sauvezie
November 1995, American journal of hematology,
Y J Bignon, and A Janin-Mercier, and J J Dubost, and J M Ristori, and Y Fonck, and J C Alphonse, and B J Sauvezie
June 1991, [Rinsho ketsueki] The Japanese journal of clinical hematology,
Copied contents to your clipboard!