Abnormal origin of right pulmonary artery from the ascending aorta in an infant ("Hemitruncus"). 2023

Alexandros Tsoutsinos, and Ioannis Germanakis, and Meletios Kanakis, and George Samanidis, and Stefanos Despotopoulos, and Theofili Kousi, and Spyridoula Katsilouli, and Olga Karapanagiotou, and Dimitrios Bobos
Department of Paediatric Cardiology and Adult Congenital Heart Disease Onassis Cardiac Surgery Centre Athens Greece.

Anomalous origin of right pulmonary artery from the ascending aorta is a rare congenital malformation and it needs surgical management. Consequences of this condition affect lead to pulmonary hypertension and severe pulmonary vascular disease. Anomalous origin of right pulmonary artery from the ascending aorta is a rare congenital heart malformation that results in early infant mortality affecting the right pulmonary artery more than the left. These patients are at risk for the early development of significant pulmonary hypertension. The surgical management during the early period of life is imperative.

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