Biomaterial Database

Progressive hemifacial atrophy (Parry-Romberg syndrome): report of two cases. 1979

T Aracena, and F P Roca, and M Barragan

We describe 2 cases of progressive hemifacial atrophy (Parry-Romberg syndrome) with typical facial and ocular involvement. Ocular manifestations in these 2 cases include enophthalmos, due to fat atrophy, decreased corneal sensitivity, episcleritis, and band keratopathy. The slowly progressive changes were documented in one case over a 40 year period. Both cases were unilateral with limitation of the lesions at the midline.

UI	MeSH Term	Description	Entries
D008297	Male		Males
D008875	Middle Aged	An adult aged 45 - 64 years.	Middle Age
D009915	Orbit	Bony cavity that holds the eyeball and its associated tissues and appendages.	Eye Socket,Eye Sockets,Orbits,Socket, Eye,Sockets, Eye
D003316	Corneal Diseases	Diseases of the cornea.	Corneal Disease,Disease, Corneal,Diseases, Corneal
D005128	Eye Diseases	Diseases affecting the eye.	Eye Disorders,Eye Disease,Eye Disorder
D005150	Facial Hemiatrophy	A syndrome characterized by slowly progressive unilateral atrophy of facial subcutaneous fat, muscle tissue, skin, cartilage, and bone. The condition typically progresses over a period of 2-10 years and then stabilizes.	Hemifacial Atrophy,Romberg Disease,Facial Hemiatrophy of Romberg,Hemifacial Atrophy, Progressive,Parry-Romberg Disease,Parry-Romberg Syndrome,Progressive Facial Hemiatrophy,Progressive Hemifacial Atrophy,Romberg Hemi-Facial Atrophy,Romberg's Disease,Atrophies, Hemifacial,Atrophies, Progressive Hemifacial,Atrophy, Hemifacial,Atrophy, Progressive Hemifacial,Atrophy, Romberg Hemi-Facial,Disease, Parry-Romberg,Disease, Romberg,Disease, Romberg's,Facial Hemiatrophies,Facial Hemiatrophies, Progressive,Facial Hemiatrophy, Progressive,Hemi-Facial Atrophy, Romberg,Hemiatrophies, Facial,Hemiatrophies, Progressive Facial,Hemiatrophy, Facial,Hemiatrophy, Progressive Facial,Hemifacial Atrophies,Parry Romberg Disease,Parry Romberg Syndrome,Progressive Facial Hemiatrophies,Progressive Hemifacial Atrophies,Romberg Facial Hemiatrophy,Romberg Hemi Facial Atrophy,Rombergs Disease,Syndrome, Parry-Romberg
D005260	Female		Females
D006801	Humans	Members of the species Homo sapiens.	Homo sapiens,Man (Taxonomy),Human,Man, Modern,Modern Man
D000273	Adipose Tissue	Specialized connective tissue composed of fat cells (ADIPOCYTES). It is the site of stored FATS, usually in the form of TRIGLYCERIDES. In mammals, there are two types of adipose tissue, the WHITE FAT and the BROWN FAT. Their relative distributions vary in different species with most adipose tissue being white.	Fatty Tissue,Body Fat,Fat Pad,Fat Pads,Pad, Fat,Pads, Fat,Tissue, Adipose,Tissue, Fatty
D000328	Adult	A person having attained full growth or maturity. Adults are of 19 through 44 years of age. For a person between 19 and 24 years of age, YOUNG ADULT is available.	Adults