Congenital anterior urethral diverticulum (CAUD) was diagnosed in 7 male subjects, of whom 3 cases were neonates, 3 cases were school aged and 1 case was adolescent. Varying degrees of urinary obstruction, often associated with urinary tract infection, were the main presenting symptoms. Urinary ascites, a rare manifestation of CAUD, was presented in a neonate associated with severe upper urinary tract changes. In 6 cases the diverticulum was of the wide-mouthed saccular type, and in 1 case of the narrow neck globular type. The clinical presentations, methods of diagnosis and the treatment modalities are discussed.