Biomaterial Database

Congenital hemihypertrophy with adrenal carcinoma and medullary sponge kidney. 1983

D C Saypol, and V P Laudone

About 230 cases of congenital hemihypertrophy have been reported. A significant number of genitourinary abnormalities have been described in association with this disorder. Among these are Wilms tumors, adrenal malignancies, and medullary sponge kidney. We report on a patient with congenital hemihypertrophy, medullary sponge kidney, and an adrenal carcinoma. A brief review of the literature is given.

UI	MeSH Term	Description	Entries
D006984	Hypertrophy	General increase in bulk of a part or organ due to CELL ENLARGEMENT and accumulation of FLUIDS AND SECRETIONS, not due to tumor formation, nor to an increase in the number of cells (HYPERPLASIA).	Hypertrophies
D007691	Medullary Sponge Kidney	A non-hereditary KIDNEY disorder characterized by the abnormally dilated (ECTASIA) medullary and inner papillary portions of the collecting ducts. These collecting ducts usually contain CYSTS or DIVERTICULA filled with jelly-like material or small calculi (KIDNEY STONES) leading to infections or obstruction. It should be distinguished from congenital or hereditary POLYCYSTIC KIDNEY DISEASES.	Cacchi Ricci Disease,Cacchi-Ricci Syndrome,Kidney, Sponge,Precalyceal Canalicular Ectasia,Cacchi Ricci Syndrome,Canalicular Ectasia, Precalyceal,Canalicular Ectasias, Precalyceal,Disease, Cacchi Ricci,Ectasia, Precalyceal Canalicular,Ectasias, Precalyceal Canalicular,Kidneys, Sponge,Medullary Sponge Kidneys,Precalyceal Canalicular Ectasias,Ricci Disease, Cacchi,Sponge Kidney,Sponge Kidney, Medullary,Sponge Kidneys,Sponge Kidneys, Medullary,Syndrome, Cacchi-Ricci
D008297	Male		Males
D002277	Carcinoma	A malignant neoplasm made up of epithelial cells tending to infiltrate the surrounding tissues and give rise to metastases. It is a histological type of neoplasm and not a synonym for "cancer."	Carcinoma, Anaplastic,Carcinoma, Spindle-Cell,Carcinoma, Undifferentiated,Carcinomatosis,Epithelial Neoplasms, Malignant,Epithelioma,Epithelial Tumors, Malignant,Malignant Epithelial Neoplasms,Neoplasms, Malignant Epithelial,Anaplastic Carcinoma,Anaplastic Carcinomas,Carcinoma, Spindle Cell,Carcinomas,Carcinomatoses,Epithelial Neoplasm, Malignant,Epithelial Tumor, Malignant,Epitheliomas,Malignant Epithelial Neoplasm,Malignant Epithelial Tumor,Malignant Epithelial Tumors,Neoplasm, Malignant Epithelial,Spindle-Cell Carcinoma,Spindle-Cell Carcinomas,Tumor, Malignant Epithelial,Undifferentiated Carcinoma,Undifferentiated Carcinomas
D006801	Humans	Members of the species Homo sapiens.	Homo sapiens,Man (Taxonomy),Human,Man, Modern,Modern Man
D000310	Adrenal Gland Neoplasms	Tumors or cancer of the ADRENAL GLANDS.	Adrenal Cancer,Adrenal Gland Cancer,Adrenal Neoplasm,Cancer of the Adrenal Gland,Neoplasms, Adrenal Gland,Adrenal Cancers,Adrenal Gland Cancers,Adrenal Gland Neoplasm,Adrenal Neoplasms,Cancer, Adrenal,Cancer, Adrenal Gland,Cancers, Adrenal,Cancers, Adrenal Gland,Neoplasm, Adrenal,Neoplasm, Adrenal Gland,Neoplasms, Adrenal
D000328	Adult	A person having attained full growth or maturity. Adults are of 19 through 44 years of age. For a person between 19 and 24 years of age, YOUNG ADULT is available.	Adults
D013577	Syndrome	A characteristic symptom complex.	Symptom Cluster,Cluster, Symptom,Clusters, Symptom,Symptom Clusters,Syndromes