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Long-term penicillamine therapy for Wilson's disease. 1980

G D Haggstrom, and B I Hirschowitz, and A Flint

UI MeSH Term Description Entries
D008297 Male Males
D010396 Penicillamine 3-Mercapto-D-valine. The most characteristic degradation product of the penicillin antibiotics. It is used as an antirheumatic and as a chelating agent in Wilson's disease. Dimethylcysteine,Mercaptovaline,beta,beta-Dimethylcysteine,Copper Penicillaminate,Cuprenil,Cuprimine,D-3-Mercaptovaline,D-Penicillamine,Metalcaptase,D 3 Mercaptovaline,D Penicillamine,Penicillaminate, Copper,beta,beta Dimethylcysteine
D006527 Hepatolenticular Degeneration A rare autosomal recessive disease characterized by the deposition of copper in the BRAIN; LIVER; CORNEA; and other organs. It is caused by defects in the ATP7B gene encoding copper-transporting ATPase 2 (EC 3.6.3.4), also known as the Wilson disease protein. The overload of copper inevitably leads to progressive liver and neurological dysfunction such as LIVER CIRRHOSIS; TREMOR; ATAXIA and intellectual deterioration. Hepatic dysfunction may precede neurologic dysfunction by several years. Cerebral Pseudosclerosis,Neurohepatic Degeneration,Pseudosclerosis,Wilson Disease,Copper Storage Disease,Hepatic Form of Wilson Disease,Hepato-Neurologic Wilson Disease,Hepatocerebral Degeneration,Hepatolenticular Degeneration Syndrome,Kinnier-Wilson Disease,Progressive Lenticular Degeneration,Westphal-Strumpell Syndrome,Wilson Disease, Hepatic Form,Wilson's Disease,Cerebral Pseudoscleroses,Copper Storage Diseases,Degeneration Syndrome, Hepatolenticular,Degeneration Syndromes, Hepatolenticular,Degeneration, Hepatocerebral,Degeneration, Hepatolenticular,Degeneration, Neurohepatic,Degeneration, Progressive Lenticular,Degenerations, Hepatocerebral,Degenerations, Neurohepatic,Disease, Copper Storage,Diseases, Copper Storage,Diseases, Hepato-Neurologic Wilson,Diseases, Kinnier-Wilson,Hepato Neurologic Wilson Disease,Hepato-Neurologic Wilson Diseases,Hepatocerebral Degenerations,Hepatolenticular Degeneration Syndromes,Kinnier Wilson Disease,Kinnier-Wilson Diseases,Lenticular Degeneration, Progressive,Neurohepatic Degenerations,Pseudoscleroses, Cerebral,Pseudosclerosis, Cerebral,Storage Disease, Copper,Storage Diseases, Copper,Syndrome, Hepatolenticular Degeneration,Syndromes, Hepatolenticular Degeneration,Westphal Strumpell Syndrome,Westphal-Strumpell Syndromes,Wilson Disease, Hepato-Neurologic,Wilson Diseases, Hepato-Neurologic,Wilsons Disease
D006801 Humans Members of the species Homo sapiens. Homo sapiens,Man (Taxonomy),Human,Man, Modern,Modern Man
D000328 Adult A person having attained full growth or maturity. Adults are of 19 through 44 years of age. For a person between 19 and 24 years of age, YOUNG ADULT is available. Adults

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G D Haggstrom, and B I Hirschowitz, and A Flint
Systemic sclerosis-like lesions during long-term penicillamine therapy for Wilson's disease.
January 1987, The British journal of dermatology,
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Ophthalmoscopic changes in a patient with Wilson's disease during long-term penicillamine therapy.
September 1978, Annals of ophthalmology,
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[Laboratory changes and complications during long-term therapy of Wilson's disease using D-penicillamine].
April 1970, Vnitrni lekarstvi,
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[Wilson's disease (experience of long-term treatment with penicillamine---con penicilamina].
June 1974, Revista clinica espanola,
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Long-term therapy of Wilson's disease.
July 1971, Annals of internal medicine,
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Penicillamine, a new oral therapy for Wilson's disease.
October 1956, The American journal of medicine,
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Penicillamine therapy for schizophreniform psychosis in Wilson's disease.
November 1985, The Journal of nervous and mental disease,
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[Presymptomatic and hepatic forms of Wilson's disease in childhood. Long-term therapy with D-penicillamine].
December 1968, Praxis,
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Resolution of cerebral white matter lesions following long-term penicillamine therapy for Wilson's disease: report of a case.
June 1992, Journal of the Formosan Medical Association = Taiwan yi zhi,
G D Haggstrom, and B I Hirschowitz, and A Flint
[Liver copper determination in long-term treatment of Wilson's disease with D-penicillamine].
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