-transparent.png){kind=logo}
Between January 1985 and January 1990, six cases of neonatal-onset chronic intestinal pseudo-obstruction syndrome (CIPS) were identified. Failure to gain weight in six cases, abdominal distention in five, and vomiting in five were the most common presenting symptoms. The contrast studies of the gastrointestinal tract demonstrated delayed transit time in 6/6, jejunal or ileal dilatation in 1/6, megaduodenum in 1/6, dilatation of the colon with barium retention in 4/6, and microcolon in 1/6. Urinary tract involvement was noted in three patients. Laparotomy, performed in three patients, revealed no mechanical obstruction. Except for hypoganglionosis in Patient 4, no recognizable neuropathy or myopathy was noted histopathologically. Four patients expired within 2 months after discharge. We conclude that CIPS with neonatal onset should be suspected when infants have urinary retention and abdominal distention or constipation beginning at birth or soon after. The prognosis of CIPS presenting in the newborn period appears worse than that presenting in childhood or adulthood.
Y C Huang, and
H C Lee, and
F Y Huang, and
H A Kao, and
M L Yeh, and
P Y Chang, and
J C Sheu, and
S L Shih, and
B F Chen
August 1995,
Muscle & nerve,
Y C Huang, and
H C Lee, and
F Y Huang, and
H A Kao, and
M L Yeh, and
P Y Chang, and
J C Sheu, and
S L Shih, and
B F Chen
November 1993,
The Journal of pediatrics,
Y C Huang, and
H C Lee, and
F Y Huang, and
H A Kao, and
M L Yeh, and
P Y Chang, and
J C Sheu, and
S L Shih, and
B F Chen
April 1982,
The West Virginia medical journal,
Y C Huang, and
H C Lee, and
F Y Huang, and
H A Kao, and
M L Yeh, and
P Y Chang, and
J C Sheu, and
S L Shih, and
B F Chen
June 1989,
Mayo Clinic proceedings,
Y C Huang, and
H C Lee, and
F Y Huang, and
H A Kao, and
M L Yeh, and
P Y Chang, and
J C Sheu, and
S L Shih, and
B F Chen
December 2020,
Terapevticheskii arkhiv,
Y C Huang, and
H C Lee, and
F Y Huang, and
H A Kao, and
M L Yeh, and
P Y Chang, and
J C Sheu, and
S L Shih, and
B F Chen
February 2007,
Revista espanola de enfermedades digestivas,
Y C Huang, and
H C Lee, and
F Y Huang, and
H A Kao, and
M L Yeh, and
P Y Chang, and
J C Sheu, and
S L Shih, and
B F Chen
June 1999,
Current treatment options in gastroenterology,
Y C Huang, and
H C Lee, and
F Y Huang, and
H A Kao, and
M L Yeh, and
P Y Chang, and
J C Sheu, and
S L Shih, and
B F Chen
February 2005,
Current treatment options in gastroenterology,
Y C Huang, and
H C Lee, and
F Y Huang, and
H A Kao, and
M L Yeh, and
P Y Chang, and
J C Sheu, and
S L Shih, and
B F Chen
June 2016,
The American surgeon,
Y C Huang, and
H C Lee, and
F Y Huang, and
H A Kao, and
M L Yeh, and
P Y Chang, and
J C Sheu, and
S L Shih, and
B F Chen
September 1992,
Deutsche medizinische Wochenschrift (1946),
