Prune-belly syndrome associated with omphalocele in a female newborn. 1995

M Güvenç, and H Güvenç, and A D Aygün, and O Yalçin, and Y C Baydinç, and F Soylu
Department of Pediatrics, Firat University of Medical Faculty, Elaziğ, Turkey.

The authors report on a female newborn with prune-belly syndrome (PBS) in association with omphalocele. This case raises the total of omphalocele associated with PBS to seven. The authors suggest that this case lends support to the concept of PBS being caused by an early disturbance of mesodermal development in both the abdominal wall and the urinary tract.

UI MeSH Term Description Entries
D007231 Infant, Newborn An infant during the first 28 days after birth. Neonate,Newborns,Infants, Newborn,Neonates,Newborn,Newborn Infant,Newborn Infants
D011535 Prune Belly Syndrome A syndrome characterized by abdominal wall musculature deficiency, cryptorchism, and urinary tract abnormalities. The syndrome derives its name from its characteristic distended abdomen with wrinkled skin. Abdominal Muscle Deficiency Syndrome,Congenital Absence of the Abdominal Muscles,Eagle-Barrett Syndrome,Obrinsky Syndrome,Prune-Belly Syndrome,Eagle Barrett Syndrome,Prune Belly Syndromes,Prune-Belly Syndromes,Syndrome, Eagle-Barrett,Syndrome, Obrinsky,Syndrome, Prune Belly,Syndrome, Prune-Belly,Syndromes, Prune Belly,Syndromes, Prune-Belly
D005260 Female Females
D006554 Hernia, Umbilical A HERNIA due to an imperfect closure or weakness of the umbilical ring. It appears as a skin-covered protrusion at the UMBILICUS during crying, coughing, or straining. The hernia generally consists of OMENTUM or SMALL INTESTINE. The vast majority of umbilical hernias are congenital but can be acquired due to severe abdominal distention. Exomphalos,Omphalocele,Umbilical Hernia,Hernias, Umbilical,Omphaloceles,Umbilical Hernias
D006801 Humans Members of the species Homo sapiens. Homo sapiens,Man (Taxonomy),Human,Man, Modern,Modern Man
D017809 Fatal Outcome Death resulting from the presence of a disease in an individual, as shown by a single case report or a limited number of patients. This should be differentiated from DEATH, the physiological cessation of life and from MORTALITY, an epidemiological or statistical concept. Fatal Outcomes,Outcome, Fatal,Outcomes, Fatal

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