Biomaterial Database

Caroli's disease with congenital hepatic fibrosis and medullary sponge kidney. 1994

A C Braga, and A Calheno, and H Rocha, and J Lourenço-Gomes

Department of Pediatric Gastroenterology, Maria Pia Children's Hospital, Oporto, Portugal.

UI	MeSH Term	Description	Entries
D007223	Infant	A child between 1 and 23 months of age.	Infants
D007691	Medullary Sponge Kidney	A non-hereditary KIDNEY disorder characterized by the abnormally dilated (ECTASIA) medullary and inner papillary portions of the collecting ducts. These collecting ducts usually contain CYSTS or DIVERTICULA filled with jelly-like material or small calculi (KIDNEY STONES) leading to infections or obstruction. It should be distinguished from congenital or hereditary POLYCYSTIC KIDNEY DISEASES.	Cacchi Ricci Disease,Cacchi-Ricci Syndrome,Kidney, Sponge,Precalyceal Canalicular Ectasia,Cacchi Ricci Syndrome,Canalicular Ectasia, Precalyceal,Canalicular Ectasias, Precalyceal,Disease, Cacchi Ricci,Ectasia, Precalyceal Canalicular,Ectasias, Precalyceal Canalicular,Kidneys, Sponge,Medullary Sponge Kidneys,Precalyceal Canalicular Ectasias,Ricci Disease, Cacchi,Sponge Kidney,Sponge Kidney, Medullary,Sponge Kidneys,Sponge Kidneys, Medullary,Syndrome, Cacchi-Ricci
D008297	Male		Males
D011859	Radiography	Examination of any part of the body for diagnostic purposes by means of X-RAYS or GAMMA RAYS, recording the image on a sensitized surface (such as photographic film).	Radiology, Diagnostic X-Ray,Roentgenography,X-Ray, Diagnostic,Diagnostic X-Ray,Diagnostic X-Ray Radiology,X-Ray Radiology, Diagnostic,Diagnostic X Ray,Diagnostic X Ray Radiology,Diagnostic X-Rays,Radiology, Diagnostic X Ray,X Ray Radiology, Diagnostic,X Ray, Diagnostic,X-Rays, Diagnostic
D006801	Humans	Members of the species Homo sapiens.	Homo sapiens,Man (Taxonomy),Human,Man, Modern,Modern Man
D014463	Ultrasonography	The visualization of deep structures of the body by recording the reflections or echoes of ultrasonic pulses directed into the tissues. Use of ultrasound for imaging or diagnostic purposes employs frequencies ranging from 1.6 to 10 megahertz.	Echography,Echotomography,Echotomography, Computer,Sonography, Medical,Tomography, Ultrasonic,Ultrasonic Diagnosis,Ultrasonic Imaging,Ultrasonographic Imaging,Computer Echotomography,Diagnosis, Ultrasonic,Diagnostic Ultrasound,Ultrasonic Tomography,Ultrasound Imaging,Diagnoses, Ultrasonic,Diagnostic Ultrasounds,Imaging, Ultrasonic,Imaging, Ultrasonographic,Imaging, Ultrasound,Imagings, Ultrasonographic,Imagings, Ultrasound,Medical Sonography,Ultrasonic Diagnoses,Ultrasonographic Imagings,Ultrasound, Diagnostic,Ultrasounds, Diagnostic
D016767	Caroli Disease	Congenital cystic dilatation of the intrahepatic bile ducts (BILE DUCTS, INTRAHEPATIC). It consists of 2 types: simple Caroli disease is characterized by bile duct dilatation (ectasia) alone; and complex Caroli disease is characterized by bile duct dilatation with extensive hepatic fibrosis and portal hypertension (HYPERTENSION, PORTAL). Benign renal tubular ectasia is associated with both types of Caroli disease.	Caroli's Disease,Caroli's Syndrome,Caroli Syndrome,Carolis Disease,Carolis Syndrome,Disease, Caroli,Disease, Caroli's,Syndrome, Caroli's

Related Publications

A C Braga, and A Calheno, and H Rocha, and J Lourenço-Gomes

A lesion resembling medullary sponge kidney in patients with congenital hepatic fibrosis.

April 1962, Clinical radiology,

A C Braga, and A Calheno, and H Rocha, and J Lourenço-Gomes

[Hepatic fibropolycystic disease (Caroli's disease and congenital hepatic fibrosis)].

January 1988, Gaceta medica de Mexico,

A C Braga, and A Calheno, and H Rocha, and J Lourenço-Gomes

Congenital hepatic fibrosis and polycystic disease of kidneys with the roentgen appearance of medullary sponge kidney.

January 1974, Birth defects original article series,

A C Braga, and A Calheno, and H Rocha, and J Lourenço-Gomes

Caroli's syndrome associated with medullary sponge kidney and nephrocalcinosis.

June 1996, Nephrology, dialysis, transplantation : official publication of the European Dialysis and Transplant Association - European Renal Association,

A C Braga, and A Calheno, and H Rocha, and J Lourenço-Gomes

[An autopsy case of congenital hepatic fibrosis and medullary sponge kidney with secondary gout].

July 1987, Nihon Naika Gakkai zasshi. The Journal of the Japanese Society of Internal Medicine,

A C Braga, and A Calheno, and H Rocha, and J Lourenço-Gomes

A Case of Congenital Hepatic Fibrosis Associated With Medullary Sponge Kidney-Radiologic and Pathologic Features.

April 2012, Gastroenterology research,

A C Braga, and A Calheno, and H Rocha, and J Lourenço-Gomes

Caroli's disease in congenital hepatic fibrosis and infantile polycystic disease.

December 1982, Liver,

A C Braga, and A Calheno, and H Rocha, and J Lourenço-Gomes

[Congenital hepatic fibrosis associated with Caroli's disease: a case report].

June 2019, Zhonghua gan zang bing za zhi = Zhonghua ganzangbing zazhi = Chinese journal of hepatology,