Biomaterial Database

Pseudoxanthoma-elasticum-like papillary dermal elastolysis: a new case. 1994

C Pirard, and F Delbrouck-Poot, and A Bourlond

Service de Dermatologie, Cliniques universitaires Saint-Luc, Bruxelles, Belgique.

We report the clinicopathological features of an old woman with a recent and progressive development of soft white-yellow papules of the neck and supraclavicular areas reminding of pseudoxanthoma elasticum without systemic involvement. The similarity of this entity with fibroelastopathic papular dermatoses of the neck is briefly discussed.

UI	MeSH Term	Description	Entries
D009333	Neck	The part of a human or animal body connecting the HEAD to the rest of the body.	Necks
D011561	Pseudoxanthoma Elasticum	An inherited disorder of connective tissue with extensive degeneration and calcification of ELASTIC TISSUE primarily in the skin, eye, and vasculature. At least two forms exist, autosomal recessive and autosomal dominant. This disorder is caused by mutations of one of the ATP-BINDING CASSETTE TRANSPORTERS. Patients are predisposed to MYOCARDIAL INFARCTION and GASTROINTESTINAL HEMORRHAGE.	Gronblad-Strandberg Syndrome,Groenblad-Strandberg Syndrome,Pseudoxanthoma Elasticum, Autosomal Dominant,Pseudoxanthoma Elasticum, Forme Fruste,Pseudoxanthoma Elasticum, Incomplete,Elasticum, Incomplete Pseudoxanthoma,Elasticums, Incomplete Pseudoxanthoma,Gronblad Strandberg Syndrome,Incomplete Pseudoxanthoma Elasticum,Incomplete Pseudoxanthoma Elasticums,Pseudoxanthoma Elasticums, Incomplete,Syndrome, Gronblad-Strandberg
D003937	Diagnosis, Differential	Determination of which one of two or more diseases or conditions a patient is suffering from by systematically comparing and contrasting results of diagnostic measures.	Diagnoses, Differential,Differential Diagnoses,Differential Diagnosis
D005260	Female		Females
D006801	Humans	Members of the species Homo sapiens.	Homo sapiens,Man (Taxonomy),Human,Man, Modern,Modern Man
D000368	Aged	A person 65 years of age or older. For a person older than 79 years, AGED, 80 AND OVER is available.	Elderly
D001415	Back	The rear surface of an upright primate from the shoulders to the hip, or the dorsal surface of tetrapods.
D017444	Skin Diseases, Papulosquamous	A group of dermatoses with distinct morphologic features. The primary lesion is most commonly a papule, usually erythematous, with a variable degree of scaling on the surface. Plaques form through the coalescing of primary lesions.	Papulosquamous Disorders,Papulosquamous Skin Diseases,Disease, Papulosquamous Skin,Diseases, Papulosquamous Skin,Disorder, Papulosquamous,Disorders, Papulosquamous,Papulosquamous Disorder,Papulosquamous Skin Disease,Skin Disease, Papulosquamous