[Two cases of Shy-Drager syndrome--clinical picture and electrophysiological findings]. 1993

M Bilińska, and M Szenborn
Katedry i Kliniki Neurologii Ak. Med., Wrocławiu.

Two cases are presented of Shy-Drager syndrome of various clinical symptomatology. The authors call attention to differential diagnosis and the usefulness of electrophysiological examinations in this syndrome. The particular diagnostic value of evoked auditory brainstem potential examination is stressed.

UI MeSH Term Description Entries
D008297 Male Males
D008875 Middle Aged An adult aged 45 - 64 years. Middle Age
D004594 Electrophysiology The study of the generation and behavior of electrical charges in living organisms particularly the nervous system and the effects of electricity on living organisms.
D006801 Humans Members of the species Homo sapiens. Homo sapiens,Man (Taxonomy),Human,Man, Modern,Modern Man
D012791 Shy-Drager Syndrome A progressive neurodegenerative condition of the central and autonomic nervous systems characterized by atrophy of the preganglionic lateral horn neurons of the thoracic spinal cord. This disease is generally considered a clinical variant of MULTIPLE SYSTEM ATROPHY. Affected individuals present in the fifth or sixth decade with ORTHOSTASIS and bladder dysfunction; and later develop FECAL INCONTINENCE; anhidrosis; ATAXIA; IMPOTENCE; and alterations of tone suggestive of basal ganglia dysfunction. (From Adams et al., Principles of Neurology, 6th ed, p536) Autonomic Failure, Progressive,Idiopathic Orthostatic Hypotension, Shy-Drager Type,Orthostatic Hypotension, Dysautonomic,Dysautonomia-Orthostatic Hypotension Syndrome,Syndrome, Dysautonomia-Orthostatic Hypotension,Autonomic Failures, Progressive,Dysautonomia Orthostatic Hypotension Syndrome,Dysautonomia-Orthostatic Hypotension Syndromes,Dysautonomic Orthostatic Hypotension,Dysautonomic Orthostatic Hypotensions,Failure, Progressive Autonomic,Failures, Progressive Autonomic,Hypotension Syndrome, Dysautonomia-Orthostatic,Hypotension Syndromes, Dysautonomia-Orthostatic,Hypotension, Dysautonomic Orthostatic,Hypotensions, Dysautonomic Orthostatic,Idiopathic Orthostatic Hypotension, Shy Drager Type,Orthostatic Hypotensions, Dysautonomic,Progressive Autonomic Failure,Progressive Autonomic Failures,Shy Drager Syndrome,Syndrome, Dysautonomia Orthostatic Hypotension,Syndrome, Shy-Drager,Syndromes, Dysautonomia-Orthostatic Hypotension
D016057 Evoked Potentials, Auditory, Brain Stem Electrical waves in the CEREBRAL CORTEX generated by BRAIN STEM structures in response to auditory click stimuli. These are found to be abnormal in many patients with CEREBELLOPONTINE ANGLE lesions, MULTIPLE SCLEROSIS, or other DEMYELINATING DISEASES. Acoustic Evoked Brain Stem Potentials,Auditory Brain Stem Evoked Responses,Brain Stem Auditory Evoked Potentials,Evoked Responses, Auditory, Brain Stem,Acoustic Evoked Brain Stem Potential,Acoustic Evoked Brainstem Potential,Acoustic Evoked Brainstem Potentials,Auditory Brain Stem Evoked Response,Auditory Brain Stem Response,Auditory Brain Stem Responses,Auditory Brainstem Evoked Response,Auditory Brainstem Evoked Responses,Auditory Brainstem Responses,Brain Stem Auditory Evoked Potential,Brainstem Auditory Evoked Potential,Brainstem Auditory Evoked Potentials,Evoked Potential, Auditory, Brainstem,Evoked Potentials, Auditory, Brainstem,Evoked Response, Auditory, Brain Stem,Evoked Response, Auditory, Brainstem,Evoked Responses, Auditory, Brainstem,Auditory Brainstem Response,Brainstem Response, Auditory,Brainstem Responses, Auditory,Response, Auditory Brainstem,Responses, Auditory Brainstem

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