OBJECTIVE Review presentation and outcome in pediatric patients identified either because of complete tracheal ring malformation or those undergoing tracheal resection or partial cricoid resection with primary tracheal anastomosis. METHODS Retrospective chart analysis in an academic tertiary referral pediatric hospital in the United States. METHODS Twenty-three children undergoing surgical repair of complete tracheal ring malformation from 1985 to 1995. Sixteen children with tracheal stenosis undergoing resection from 1984 to 1995. RESULTS In patients with complete tracheal rings the mortality rate is 39% (9/23) with 47% (11/23) now extubated. The recent mortality rate is 25% (2/8) with 62% (5/8) now extubated. Sixteen patients underwent tracheal resection or cricotracheal resection. Twelve patients had tracheal resection with primary tracheal anastomosis. Eleven of these are now decannulated (92%). Four patients underwent partial cricoid resection with primary thyrotracheal anastomosis. All of these patients are decannulated without need for further surgery (100%).