Biomaterial Database

Otorhinolaryngological complications of progressive facial hemiatrophy (Romberg's disease). 1995

C Matthias, and K Terstegge, and H Siemes

Department of Otorhinolaryngology, Virchow Hospital of Humboldt University, Berlin, Germany.

Progressive facial hemiatrophy (PFH) is characterized by slowly progressive atrophy of subcutaneous tissue. Bone, muscles, nerves, the eye, and the brain may be affected by atrophy. Four patients suffering from various otorhinolaryngological complications of PFH or Romberg's disease are reported. Unilateral hearing loss could be located in the inner ear of one patient by audiologic examination. Localized bone destruction and disintegration of a portion of the anterior wall of the frontal sinus were observed in a patient after more than three decades. Marked shrinking of the homolateral parotid gland and homolateral masticatory spasm are reported as further otorhinolaryngological manifestations. The various complications of PFH call for close interdisciplinary cooperation.

UI	MeSH Term	Description	Entries
D007758	Ear, Inner	The essential part of the hearing organ consists of two labyrinthine compartments: the bony labyrinthine and the membranous labyrinth. The bony labyrinth is a complex of three interconnecting cavities or spaces (COCHLEA; VESTIBULAR LABYRINTH; and SEMICIRCULAR CANALS) in the TEMPORAL BONE. Within the bony labyrinth lies the membranous labyrinth which is a complex of sacs and tubules (COCHLEAR DUCT; SACCULE AND UTRICLE; and SEMICIRCULAR DUCTS) forming a continuous space enclosed by EPITHELIUM and connective tissue. These spaces are filled with LABYRINTHINE FLUIDS of various compositions.	Labyrinth,Bony Labyrinth,Ear, Internal,Inner Ear,Membranous Labyrinth,Bony Labyrinths,Ears, Inner,Ears, Internal,Inner Ears,Internal Ear,Internal Ears,Labyrinth, Bony,Labyrinth, Membranous,Labyrinths,Labyrinths, Bony,Labyrinths, Membranous,Membranous Labyrinths
D008297	Male		Males
D008410	Masticatory Muscles	Muscles arising in the zygomatic arch that close the jaw. Their nerve supply is masseteric from the mandibular division of the trigeminal nerve. (From Stedman, 25th ed)	Masticatory Muscle,Muscle, Masticatory,Muscles, Masticatory
D008875	Middle Aged	An adult aged 45 - 64 years.	Middle Age
D010306	Parotid Gland	The largest of the three pairs of SALIVARY GLANDS. They lie on the sides of the FACE immediately below and in front of the EAR.	Gland, Parotid,Glands, Parotid,Parotid Glands
D002648	Child	A person 6 to 12 years of age. An individual 2 to 5 years old is CHILD, PRESCHOOL.	Children
D005150	Facial Hemiatrophy	A syndrome characterized by slowly progressive unilateral atrophy of facial subcutaneous fat, muscle tissue, skin, cartilage, and bone. The condition typically progresses over a period of 2-10 years and then stabilizes.	Hemifacial Atrophy,Romberg Disease,Facial Hemiatrophy of Romberg,Hemifacial Atrophy, Progressive,Parry-Romberg Disease,Parry-Romberg Syndrome,Progressive Facial Hemiatrophy,Progressive Hemifacial Atrophy,Romberg Hemi-Facial Atrophy,Romberg's Disease,Atrophies, Hemifacial,Atrophies, Progressive Hemifacial,Atrophy, Hemifacial,Atrophy, Progressive Hemifacial,Atrophy, Romberg Hemi-Facial,Disease, Parry-Romberg,Disease, Romberg,Disease, Romberg's,Facial Hemiatrophies,Facial Hemiatrophies, Progressive,Facial Hemiatrophy, Progressive,Hemi-Facial Atrophy, Romberg,Hemiatrophies, Facial,Hemiatrophies, Progressive Facial,Hemiatrophy, Facial,Hemiatrophy, Progressive Facial,Hemifacial Atrophies,Parry Romberg Disease,Parry Romberg Syndrome,Progressive Facial Hemiatrophies,Progressive Hemifacial Atrophies,Romberg Facial Hemiatrophy,Romberg Hemi Facial Atrophy,Rombergs Disease,Syndrome, Parry-Romberg
D005260	Female		Females
D005626	Frontal Sinus	One of the paired, but seldom symmetrical, air spaces located between the inner and outer compact layers of the FRONTAL BONE in the forehead.	Agger Nasi Cell,Frontal Recess,Frontal Sinus Ostium,Agger Nasi Cells,Cell, Agger Nasi,Frontal Recesses,Frontal Sinus Ostiums,Recess, Frontal,Sinus Ostium, Frontal,Sinus Ostiums, Frontal,Sinus, Frontal
D006311	Hearing Disorders	Conditions that impair the transmission of auditory impulses and information from the level of the ear to the temporal cortices, including the sensorineural pathways.	Distorted Hearing,Dysacusis,Paracousis,Paracusis,Hearing Disorder,Hearing, Distorted