Biomaterial Database

[Porokeratosis plantaris, palmaris et disseminataa with multiple filiform hyperkeratoses and nail dystrophy]. 1995

P H Itin

Dermatologische Universitätsklinik, Basel.

We report on a family with porokeratosis plantaris, palmaris et disseminata with a very unusual clinical manifestation. The father showed an association of multiple filiform hyperkeratosis on the trunk with sparing of the palms and soles. In addition, this patient featured secondary nail dystrophy owing to porokeratosis. The daughter had an unusual course: the disease started on the trunk and did not spread to the palms and soles until later. In general the reverse is true.

UI	MeSH Term	Description	Entries
D007642	Keratosis	Any horny growth such as a wart or callus.	Keratoderma Blennorrhagicum,Keratoma,Keratosis Blennorrhagica,Blennorrhagica, Keratosis,Blennorrhagicas, Keratosis,Blennorrhagicum, Keratoderma,Blennorrhagicums, Keratoderma,Keratoderma Blennorrhagicums,Keratomas,Keratoses,Keratosis Blennorrhagicas
D008297	Male		Males
D008875	Middle Aged	An adult aged 45 - 64 years.	Middle Age
D009260	Nail Diseases	Diseases of the nail plate and tissues surrounding it. The concept is limited to primates.	Disease, Nail,Diseases, Nail,Nail Disease
D006801	Humans	Members of the species Homo sapiens.	Homo sapiens,Man (Taxonomy),Human,Man, Modern,Modern Man
D001706	Biopsy	Removal and pathologic examination of specimens from the living body.	Biopsies
D012867	Skin	The outer covering of the body that protects it from the environment. It is composed of the DERMIS and the EPIDERMIS.
D017499	Porokeratosis	A heritable disorder of faulty keratinization characterized by the proliferation of abnormal clones of KERATINOCYTES and lesions showing varying atrophic patches surrounded by an elevated, keratotic border. These keratotic lesions can progress to overt cutaneous neoplasm. Several clinical variants are recognized, including porokeratosis of Mibelli, linear porokeratosis, disseminated superficial actinic porokeratosis, palmoplantar porokeratosis, and punctate porokeratosis.	Porokeratosis Palmaris et Plantaris Disseminata,Porokeratosis of Mibelli,Porokeratosis, Disseminated Superficial Actinic,Porokeratosis, Linear,Porokeratosis, Mibelli,Porokeratosis, Palmoplantar,Porokeratosis, Punctate,Disseminated Superficial Actinic Porokeratosis,Keratoderma Palmoplantar, Punctate Type 2,Porokeratosis Plantaris Palmaris et Disseminata,Porokeratosis Plantaris, Palmaris, Et Disseminata,Porokeratosis, Disseminated Superficial Actinic 2,Porokeratosis, Disseminated Superficial Actinic, 2,Porokeratosis, Palmar, Plantar, And Disseminated 1,Type 2 Punctate PPK,Linear Porokeratosis,Mibelli Porokeratosis,Palmoplantar Porokeratosis,Punctate Porokeratosis